Department of Orthopaedics and Sports Medicine, Seattle Children's Hospital, Seattle, Washington.
Department of Pulmonary and Sleep Medicine, Seattle Children's Hospital, Seattle, Washington.
JBJS Case Connect. 2024 Oct 24;14(4). doi: 10.2106/JBJS.CC.24.00256. eCollection 2024 Oct 1.
We describe treatment of severe multilevel congenital thoracic fusion in a 3-year-old girl with Apert Syndrome by posterior element excision, posterior column osteotomies, and gradual distraction with magnetically controlled growing rods (MCGR) with 3-year follow-up. We also describe short-term follow-up with similar management in an 8-year-old patient with a congenitally fused thoracic spine from Jarcho-Levin syndrome.
Posterior element resection and targeted posterior column osteotomies combined with gradual distraction with MCGR offers a promising treatment course for children with severe thoracic insufficiency syndrome derived from congenital fusions.
我们描述了一例 3 岁患有尖颅-多指(趾)综合征的女孩的严重多节段先天性胸段融合的治疗方法,通过后路切除、后柱截骨术和使用磁控生长棒(MCGR)进行逐渐牵引,随访 3 年。我们还描述了一例 8 岁患有先天性胸段融合的 Jarcho-Levin 综合征患者采用类似方法进行短期随访的结果。
后路切除和有针对性的后柱截骨术联合 MCGR 逐渐牵引为先天性融合导致的严重胸段发育不良综合征患儿提供了一种有前景的治疗方法。