Ciraldo A V, Platt M S, Agamanolis D P, Boeckman C R
J Pediatr Surg. 1986 Jan;21(1):49-52. doi: 10.1016/s0022-3468(86)80653-4.
The occurrence of sacrococcygeal myxopapillary ependymal tissue appears to be exceedingly rare. We report on five cases of this lesion in infants, four of which occurred in the first year of life. These cases, the youngest on record, should be added to the thirteen cases previously reported. The lesions were completely removed, and the patients have been followed without recurrence for five months to six years. These lesions arise from the coccygeal medullary vestige, which corresponds to the original site of the final closure of the posterior neuropore. The unique embryology of this region can account for the presence of sacrococcygeal teratomas, lipomas, chordomas, as well as the above described lesion. The presence of ependymal rests, as described by Bale, in most patients with postanal dimples, suggests that the incidence of this lesion should be greater. This lesion has a potential for lymph node and pulmonary metastasis and when clinically palpable, should be completely excised.
骶尾部黏液乳头状室管膜组织的出现似乎极为罕见。我们报告了5例婴儿期的这种病变，其中4例发生在出生后的第一年。这些病例是有记录以来最年轻的，应加入之前报告的13例病例中。病变均被完全切除，患者随访5个月至6年无复发。这些病变起源于尾髓遗迹，其对应于后神经孔最终闭合的原始部位。该区域独特的胚胎学可以解释骶尾部畸胎瘤、脂肪瘤、脊索瘤以及上述病变的存在。如贝尔所描述的，大多数有肛门后凹的患者存在室管膜残余，这表明该病变的发生率应该更高。这种病变有发生淋巴结和肺转移的可能，当临床上可触及肿块时，应将其完全切除。
