Department of Neurology, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, Karnataka, India-576104
Department of Neurology, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, Karnataka, India-576104.
BMJ Case Rep. 2024 Oct 23;17(10):e260606. doi: 10.1136/bcr-2024-260606.
Vertebrobasilar dolichoectasia (VBD) is a rare condition characterised by ectasia, elongation and tortuosity in the vertebrobasilar arteries. VBD prevalence ranges from 0.05% to 18%. A possible interplay between vascular risk factors and a predisposing genotype could alter the balance between tunica media matrix metalloproteinases and antiprotease activity. VBD is characterised by the disruption of smooth muscle atrophy, reticular fibre degeneration and multiple gaps in the inner elastic lamina, causing thinning of the tunica media and arterial wall weakening and deformation. VBD can be asymptomatic. VBD is often characterised by ischaemic stroke, intracerebral haemorrhage, brainstem/cranial nerve compression and subarachnoid haemorrhage. Vascular events are the most common clinical manifestation. Slow arterial blood flow results in hyperintense vascular signals, which are linked with a larger infarct and a higher risk of cerebral bleeding. Treatment for VBD is difficult. Currently, there are no specific treatments for VBD, and the available treatments focus on the consequences.
椎基底动脉延长扩张症(VBD)是一种罕见的疾病,其特征为椎基底动脉的扩张、延长和迂曲。VBD 的患病率在 0.05%至 18%之间。血管危险因素和易感基因型之间的可能相互作用可能会改变中膜基质金属蛋白酶和抗蛋白酶活性之间的平衡。VBD 的特征是平滑肌萎缩、网状纤维退化和内弹性层多处断裂,导致中膜变薄、动脉壁变弱和变形。VBD 可能无症状。VBD 常表现为缺血性卒中、脑出血、脑干/颅神经压迫和蛛网膜下腔出血。血管事件是最常见的临床表现。缓慢的动脉血流导致血管信号高信号,与更大的梗死和更高的脑出血风险相关。VBD 的治疗很困难。目前,VBD 尚无特定的治疗方法,现有的治疗方法主要针对其后果。