Baker Hannah, Rich Mark, Miller Javier, Wiegand Lucas R
Urology Department at Orlando Health, Florida International University, Herbert Wertheim College of Medicine, Miami, USA.
Pediatric Urology, Orlando Health Arnold Palmer Hospital for Children, Orlando, USA.
Cureus. 2024 Sep 25;16(9):e70162. doi: 10.7759/cureus.70162. eCollection 2024 Sep.
Ejaculatory dysfunction in adult males with bladder exstrophy-epispadias complex can occur from associated genitourinary anomalies, surgical iatrogenic scarring, infection, obstruction, and neurologic and functional causes. This case presents a 30-year-old male patient with a history of bladder exstrophy reconstruction (bladder neck closure and appendicovesicostomy) who presented with a nine-year history of intermittent perineal scrotal pain, swelling, and intermittent urethral discharge. He presented with a tender palpable perineal mass ("semen-oma"). Examination under anesthesia and endoscopy of the urethra demonstrated a distal anterior penile and proximal urethral stricture at the level of the bladder neck level from previous surgical exstrophy reconstructive procedures. Aspiration of the mass revealed a thick viscous fluid suggestive of semen. Intraoperative endoscopic evaluation and radiographic imaging revealed a distal penile urethra stricture and proximal bladder neck closure from previous genitourinary reconstruction with sequestration of semen in the ectatic urethra with reflux into the seminal vesicle. A proximal ventral penile urethrostomy was performed to allow for permanent drainage of the sequestered semen collection and future antegrade ejaculation. The postoperative course was uneventful. This case highlights the potential for sexual ejaculatory dysfunction and the need for long-term and transitional urologic care in patients with a history of complex exstrophy reconstruction.
膀胱外翻-尿道上裂综合征成年男性的射精功能障碍可能由相关的泌尿生殖系统异常、手术医源性瘢痕形成、感染、梗阻以及神经和功能原因引起。本病例介绍了一名30岁男性患者,有膀胱外翻重建病史(膀胱颈闭合和阑尾膀胱造口术),出现间歇性会阴部阴囊疼痛、肿胀及间歇性尿道分泌物9年。他有一个可触及的会阴部压痛肿块(“精液瘤”)。麻醉下检查及尿道内镜检查显示,由于既往膀胱外翻重建手术,在膀胱颈水平存在阴茎前段远端和尿道近端狭窄。肿块抽吸物显示为浓稠液体,提示为精液。术中内镜评估及影像学检查显示,既往泌尿生殖系统重建导致阴茎远端尿道狭窄及近端膀胱颈闭合,精液潴留在扩张的尿道内并反流至精囊。行近端阴茎腹侧尿道造口术,以实现潴留在体内的精液永久性引流及未来的顺行射精。术后过程顺利。本病例强调了复杂膀胱外翻重建病史患者发生性射精功能障碍的可能性以及长期和过渡性泌尿外科护理的必要性。