Medical College, Aga Khan University Medical College, Karachi, Sindh, Pakistan
Histopathology, Aga Khan University Hospital, Karachi, Sindh, Pakistan.
BMJ Case Rep. 2024 Oct 30;17(10):e260656. doi: 10.1136/bcr-2024-260656.
Bronchopulmonary sequestration is a rare condition characterised by the presence of nonfunctional, dysplastic lung tissue. This tissue receives blood supply from the systemic circulation. In this case report, we document an exceptional presentation of a woman in her 50s where bronchopulmonary sequestration in the right upper lung lobe led to haemoptysis. This sequestration received blood supply from a pulmonary artery branch, which is unusual and contrary to the usual systemic circulation. The patient underwent a right upper lobectomy, which confirmed the diagnosis of pulmonary sequestration on histopathology. The unique vascular supply and location of this case challenge conventional diagnostic and management approaches. It emphasises the necessity for meticulous evaluation and consideration of alternative vascular sources in bronchopulmonary sequestration cases.
支气管肺隔离症是一种罕见的疾病,其特征是存在无功能、发育不良的肺组织。这些组织接受体循环的血液供应。在本病例报告中,我们记录了一位 50 多岁女性的特殊表现,其右上肺叶的支气管肺隔离症导致咯血。该隔离症接受了肺动脉分支的血液供应,这是不常见的,与通常的体循环相反。患者接受了右上肺叶切除术,组织病理学证实了肺隔离症的诊断。该病例独特的血管供应和位置挑战了传统的诊断和管理方法。它强调了在支气管肺隔离症病例中需要仔细评估和考虑替代血管来源的必要性。