Alrasheed Abdulrahim S, Aldandan Ibrahim M, Noor Sadaf, Al-Schameri Abdulrahman
Department of Neurosurgery, College of Medicine, King Faisal University, AlAhsa, SAU.
Department of Laboratory Medicine, Almoosa Specialist Hospital, AlAhsa, SAU.
Cureus. 2024 Sep 30;16(9):e70539. doi: 10.7759/cureus.70539. eCollection 2024 Sep.
Intravascular papillary endothelial hyperplasia (IPEH), or Masson's tumor, is a benign vascular mass that is often misdiagnosed due to its nonspecific clinical signs. The majority of IPEH cases involve blood vessel thrombosis. Although it is a rare tumor, IPEH requires an accurate diagnosis to avoid unnecessary treatment. Overall, the tumor generally has a good prognosis. In this case report, a 16-year-old male with a known four-year history of right wrist swelling and digit numbness presented to the outpatient clinic due to worsening pain and swelling for the previous month. Based on the physical examination and radiological examination, our preliminary diagnosis was either schwannoma or neurofibroma, for which a total surgical excision was done. Postoperatively, the tumor was examined histologically and revealed a benign vascular lesion with no atypical features, which were consistent with IPEH. To prevent unnecessary invasive operations and radiation, surgeons must be aware of this rare tumor. The following case report emphasizes the importance of differentiation between Masson`s hemangioma and other similar tumors to prevent unnecessary invasive operations and radiation.
血管内乳头状内皮增生(IPEH),即马松瘤,是一种良性血管性肿物,因其临床症状不具特异性,常被误诊。大多数IPEH病例与血管血栓形成有关。尽管它是一种罕见肿瘤,但IPEH需要准确诊断以避免不必要的治疗。总体而言,该肿瘤预后通常良好。在本病例报告中,一名16岁男性,已知有右手腕肿胀和手指麻木四年病史,因前一个月疼痛和肿胀加重而到门诊就诊。根据体格检查和影像学检查,我们初步诊断为神经鞘瘤或神经纤维瘤,并进行了手术全切。术后,对肿瘤进行组织学检查,显示为良性血管病变,无异常特征,符合IPEH。为避免不必要的侵入性手术和放疗,外科医生必须了解这种罕见肿瘤。以下病例报告强调了区分马松血管瘤与其他类似肿瘤以避免不必要的侵入性手术和放疗的重要性。