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慢性血栓栓塞性肺动脉高压还是纤维性纵隔炎?

Chronic Thromboembolic Pulmonary Artery Hypertension or Fibrosing Mediastinitis?

作者信息

Kadiyani Lamk, Karuru Umadevi, Kothari Shyam Sunder, Ramakrishnan Sivasubramanian, Gupta Saurabh Kumar, Devagouru Velayudham, Patel Chetan D

机构信息

Department of Cardiology, All India Institute of Medical Sciences, Delhi, India.

Department of Cardiac, Thoracic and Vascular Surgery, All India Institute of Medical Sciences, Delhi, India.

出版信息

JACC Case Rep. 2024 Oct 2;29(19):102569. doi: 10.1016/j.jaccas.2024.102569.

DOI:10.1016/j.jaccas.2024.102569
PMID:39484314
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11522728/
Abstract

We report a case of pulmonary hypertension in association with right heart thrombus and mediastinal lymphadenopathy leading to the diagnostic dilemma of chronic thromboembolic pulmonary hypertension vs fibrosing mediastinitis despite of extensive noninvasive workup, considering different treatment strategies and therapeutic implications. Surgical findings provided a conclusive diagnosis and excellent prognosis.

摘要

我们报告一例伴有右心血栓和纵隔淋巴结肿大的肺动脉高压病例,尽管进行了广泛的无创检查,但仍导致了慢性血栓栓塞性肺动脉高压与纤维性纵隔炎的诊断困境,同时考虑了不同的治疗策略和治疗意义。手术结果提供了确定性诊断和良好的预后。

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本文引用的文献

1
Chronic thromboembolic pulmonary hypertension: realising the potential of multimodal management.慢性血栓栓塞性肺动脉高压:实现多模式管理的潜力。
Lancet Respir Med. 2023 Sep;11(9):836-850. doi: 10.1016/S2213-2600(23)00292-8. Epub 2023 Aug 14.
2
Pulmonary Hypertension Caused by Fibrosing Mediastinitis.纤维性纵隔炎所致肺动脉高压
JACC Asia. 2022 May 17;2(3):218-234. doi: 10.1016/j.jacasi.2021.11.016. eCollection 2022 Jun.
3
Riociguat in children with pulmonary arterial hypertension: The PATENT-CHILD study.利奥西呱用于儿童肺动脉高压:PATENT-CHILD研究
Pulm Circ. 2022 Jul 1;12(3):e12133. doi: 10.1002/pul2.12133. eCollection 2022 Jul.
4
Right heart thrombi (RHT) and clot in transit with concomitant PE management: Approach and considerations.右心血栓(RHT)及合并肺栓塞时的移行性血栓处理:方法与注意事项
Pulm Circ. 2022 Apr 25;12(2):e12080. doi: 10.1002/pul2.12080. eCollection 2022 Apr.
5
Investigation of two general venous thromboembolism risk-stratification models in predicting venous thromboembolic events in TB patients.两种一般静脉血栓栓塞风险分层模型在预测结核病患者静脉血栓栓塞事件中的研究。
Int J Mycobacteriol. 2022 Jan-Mar;11(1):83-87. doi: 10.4103/ijmy.ijmy_252_21.
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Chronic Thromboembolic Pulmonary Hypertension: An Update.慢性血栓栓塞性肺动脉高压:最新进展
Diagnostics (Basel). 2022 Jan 19;12(2):235. doi: 10.3390/diagnostics12020235.
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Characterisation of paediatric pulmonary hypertensive vascular disease from the PPHNet Registry.PPHNet 注册研究中儿童肺动脉高压血管疾病的特征。
Eur Respir J. 2021 Dec 31;59(1). doi: 10.1183/13993003.03337-2020. Print 2022 Jan.