Instituto Cajal, CSIC, Madrid, Spain.
Departamento de Química Física Aplicada, Universidad Autónoma de Madrid, Madrid, Spain.
Cell Mol Life Sci. 2024 Nov 1;81(1):444. doi: 10.1007/s00018-024-05485-9.
Alzheimer´s disease (AD) is characterized by neuronal function loss and degeneration. The integrity of the axon initial segment (AIS) is essential to maintain neuronal function and output. AIS alterations are detected in human post-mortem AD brains and mice models, as well as, neurodevelopmental and mental disorders. However, the mechanisms leading to AIS deregulation in AD and the extrinsic glial origin are elusive. We studied early postnatal differences in AIS cellular/molecular mechanisms in wild-type or APP/PS1 mice and combined neuron-astrocyte co-cultures. We observed AIS integrity alterations, reduced ankyrinG expression and shortening, in APP/PS1 mice from P21 and loss of AIS integrity at 21 DIV in wild-type and APP/PS1 neurons in the presence of APP/PS1 astrocytes. AnkyrinG decrease is due to mRNAs and protein reduction of retinoic acid synthesis enzymes Rdh1 and Aldh1b1, as well as ADNP (Activity-dependent neuroprotective protein) in APP/PS1 astrocytes. This effect was mimicked by wild-type astrocytes expressing ADNP shRNA. In the presence of APP/PS1 astrocytes, wild-type neurons AIS is recovered by inhibition of retinoic acid degradation, and Adnp-derived NAP peptide (NAPVSIPQ) addition or P2X7 receptor inhibition, both regulated by retinoic acid levels. Moreover, P2X7 inhibitor treatment for 2 months impaired AIS disruption in APP/PS1 mice. Our findings extend current knowledge on AIS regulation, providing data to support the role of astrocytes in early postnatal AIS modulation. In conclusion, AD onset may be related to very early glial cell alterations that induce AIS and neuronal function changes, opening new therapeutic approaches to detect and avoid neuronal function loss.
阿尔茨海默病(AD)的特征是神经元功能丧失和退化。轴突起始段(AIS)的完整性对于维持神经元功能和输出至关重要。在人类 AD 大脑和小鼠模型中,以及神经发育和精神障碍中,都检测到 AIS 的改变。然而,导致 AD 中 AIS 失调的机制以及外在的神经胶质来源尚不清楚。我们研究了野生型或 APP/PS1 小鼠和神经元-星形胶质细胞共培养物中早期 postnatal AIS 细胞/分子机制的差异。我们观察到,APP/PS1 小鼠从 P21 开始 AIS 完整性发生改变,ankyrinG 表达减少和缩短,而在 APP/PS1 星形胶质细胞存在的情况下,野生型和 APP/PS1 神经元在 21 DIV 时 AIS 完整性丧失。ankyrinG 的减少是由于 APP/PS1 星形胶质细胞中 retinoic acid 合成酶 Rdh1 和 Aldh1b1 以及 ADNP(Activity-dependent neuroprotective protein)的 mRNA 和蛋白减少所致。野生型星形胶质细胞表达 ADNP shRNA 可模拟这种效应。在 APP/PS1 星形胶质细胞存在的情况下,通过抑制 retinoic acid 降解、添加 ADNP 衍生的 NAP 肽(NAPVSIPQ)或抑制 P2X7 受体,恢复野生型神经元 AIS,这两种方法都受 retinoic acid 水平的调节。此外,用 P2X7 抑制剂治疗 2 个月可改善 APP/PS1 小鼠 AIS 的破坏。我们的研究结果扩展了对 AIS 调节的现有认识,提供了数据支持星形胶质细胞在早期 postnatal AIS 调节中的作用。总之,AD 的发病可能与导致 AIS 和神经元功能改变的早期胶质细胞改变有关,为检测和避免神经元功能丧失开辟了新的治疗方法。