van Wijk Monica, van Rensburg Leon Janse, Berndorfler Bianca D, Opperman Johan F, Grobbelaar Johan, Afrogheh Amir H, Versveld Sarah, Davis Razaan
Division of Radiodiagnosis, Department of Medical Imaging and Clinical Oncology, Faculty of Medicine and Health Sciences, Stellenbosch University and Tygerberg Hospital, Cape Town, South Africa.
Nuclear Medicine Division, Department of Medical Imaging and Clinical Oncology, Faculty of Medicine and Health Sciences, Stellenbosch University and Tygerberg Hospital, Cape Town, South Africa.
SA J Radiol. 2024 Oct 22;28(1):2975. doi: 10.4102/sajr.v28i1.2975. eCollection 2024.
Phosphaturic mesenchymal tumours (PMT) are rare, benign lesions and the most common tumour to cause tumour-induced osteomalacia (TIO), a paraneoplastic syndrome. Patients frequently exhibit severe osteomalacia, accompanied by multiple fractures, which significantly impair their quality of life. Complete surgical resection is curative.
A rare case of sinonasal PMT is presented, with a focus on the imaging findings and role of the radiologist and nuclear physician.
磷尿性间叶肿瘤(PMT)是罕见的良性病变,是导致肿瘤性骨软化症(TIO)这一肿瘤旁分泌综合征的最常见肿瘤。患者常表现出严重的骨软化症,并伴有多处骨折,这显著损害了他们的生活质量。完整的手术切除可治愈。
本文报告了一例罕见的鼻窦PMT病例,重点关注影像学表现以及放射科医生和核医学医生的作用。