From the Department of Special Surgery (Samarah, Yasin), School of Medicine; from the School of Medicine (Odeh, Alkhadire, Abu Hejleh, Diab, Yousef, Abu Halaweh), University of Jordan, Amman, Jordan, and from the Sarcoma and Complex Joints Unit (Hammad), Royal National Orthopedic Hospital, Stanmore, London.
Saudi Med J. 2024 Nov;45(11):1265-1269. doi: 10.15537/smj.2024.45.11.20240602.
To review the types of upper limb congenital differences in patients seen in a tertiary hospital in Jordan and to evaluate the effectiveness of the Oberg-Manske-Tonkin (OMT) system.
The medical charts and the X-rays of 222 patients with upper limb congenital differences were reviewed. All these cases were categorized using the OMT classification system.
A careful review of the medical charts identified 222 patients with 295 upper extremity anomalies. The prevalence was 45/10000 patients. The mean age of the patients was 6.18±5.5 years, with a higher prevalence in males 54.1%. most cases were malformations 176 (79%) and of these the radial polydactyly was the most common (18.5%). A total of 28 cases of dysplasia were identified. A total of 15 (6.7%) patients were diagnosed with syndromes, of which Poland syndrome showed the highest frequency at 2.3% of the total. The least presentation was for the deformation anomalies (1.4%).
The malformation category constituted most of the congenital upper extremity difference in this study. Radial polydactyly was the most common in this category. Considering the regional differences, the need for a well-established healthcare infrastructure is a vital step toward managing and improving the outcomes of these patients.
回顾在约旦一家三级医院就诊的上肢先天性差异患者的类型,并评估 Oberg-Manske-Tonkin(OMT)系统的有效性。
回顾了 222 例上肢先天性差异患者的病历和 X 光片。所有这些病例均使用 OMT 分类系统进行分类。
仔细审查病历后,共发现 222 例 295 例上肢畸形。患病率为 45/10000 例。患者的平均年龄为 6.18±5.5 岁,男性患病率较高(54.1%)。大多数病例为畸形 176 例(79%),其中桡侧多指畸形最常见(18.5%)。共发现 28 例发育不良病例。共诊断出 15 例(6.7%)综合征患者,其中波兰综合征占总数的 2.3%,发病率最高。变形畸形的发生率最低(1.4%)。
在这项研究中,畸形类别构成了上肢先天性差异的主要类型。在该类别中,桡侧多指畸形最为常见。考虑到区域差异,建立完善的医疗保健基础设施是管理和改善这些患者预后的重要步骤。