Sah Anjali, Triveni G S, Chandrashekhara S H
Department of Radio-Diagnosis, IRCH, All India Institute of Medical Sciences, New Delhi, 110029 India.
Department of Obstetrics and Gynecology, Lady Hardinge Medical College, All New Delhi, India.
Indian J Surg Oncol. 2024 Dec;15(4):640-645. doi: 10.1007/s13193-024-01958-2. Epub 2024 May 21.
Primary inferior vena cava(IVC) leiomyosarcoma (LMS) is an extremely rare retroperitoneal mesenchymal tumour with < 500 cases reported in literature so far. Patients always present with nonspecific complaints, hence delaying the actual diagnosis, and they are associated with poor oncological outcomes. Differentiating primary leiomyosarcoma from other pathologies affecting IVC-like bland thrombus, retroperitoneal liposarcomas and other tumours infiltrating IVC secondarily may be difficult at times. We present here our experience with five cases of IVC leiomyosarcoma, who presented to us during a 6-year period.
原发性下腔静脉平滑肌肉瘤是一种极为罕见的腹膜后间叶组织肿瘤，迄今为止，文献报道的病例不足500例。患者通常表现为非特异性症状，从而延误了实际诊断，且其肿瘤学预后较差。有时，将原发性平滑肌肉瘤与其他累及下腔静脉的病变（如单纯血栓、腹膜后脂肪肉瘤及其他继发性侵犯下腔静脉的肿瘤）相鉴别可能存在困难。在此，我们介绍6年间收治的5例下腔静脉平滑肌肉瘤患者的诊疗经验。
