Markhede G, Lundgren L, Bjurstam N, Berlin O, Stener B
Acta Orthop Scand. 1986 Feb;57(1):1-7. doi: 10.3109/17453678608993204.
A follow-up study of 53 patients with extra-abdominal desmoid tumor is presented. Fine-needle aspiration biopsy seemed to be valuable in the differentiation between a desmoid tumor and a truly malignant soft tissue tumor. The angiographic pictures did not differ from those of other soft tissue tumors, but valuable topographic information was obtained from the angiography in the preoperative planning. The overall local recurrence rate was 17/44, and 15 of the recurrences occurred within the first 2 years. Complete removal of the affected muscle or muscle group is recommended. Local control can be achieved by non-ablative surgery even after multiple recurrences. Only one out of 53 patients died of the tumor disease. Radiotherapy can be attempted in extensive tumors, and amputation should be reserved for tumors which have failed to respond to this treatment.
本文介绍了一项对53例腹外硬纤维瘤患者的随访研究。细针穿刺活检在区分硬纤维瘤和真正的恶性软组织肿瘤方面似乎很有价值。血管造影图像与其他软组织肿瘤的图像并无差异，但在术前规划中，血管造影可提供有价值的局部信息。总体局部复发率为17/44，其中15例复发发生在头两年内。建议彻底切除受影响的肌肉或肌肉群。即使在多次复发后，非切除性手术也可实现局部控制。53例患者中只有1例死于肿瘤疾病。对于广泛的肿瘤可尝试放疗，截肢应保留用于对该治疗无反应的肿瘤。
