Zhu Xian-Hui, Zhou Ya-Ping, Zhang Qiao, Zhu Ming-Yi, Song Xiao-Wei, Li Jun, Chen Jiang, Shi Yun, Sun Kang-Jian, Zhang Yong-Jie, Zhang Jing, Xia Tian, Huang Bao-Sheng, Meng Fan, Zhou Qi-Gang
Department of Clinical Pharmacology, School of Pharmacy, Nanjing Medical University, Nanjing, 211166, China.
Sir Run Run Hospital, Nanjing Medical University, Nanjing, 211166, China.
EMBO Mol Med. 2025 Jan;17(1):85-111. doi: 10.1038/s44321-024-00168-1. Epub 2024 Dec 9.
The molecular mechanism underlying the role of hippocampal hilar interneuron degeneration in temporal lobe epilepsy (TLE) remains unclear. Especially, very few studies have focused on the role of neuronal nitric oxide synthase (nNOS, encoded by Nos1) containing hilar interneurons in TLE. In the present study, Nos1 conditional knockout mice were constructed, and we found that selective deletion of Nos1 in hilar interneurons rather than dentate granular cells (DGCs) triggered epileptogenesis. The level of nNOS was downregulated in patients and mice with TLE. Nos1 deletion led to excessive epilepsy-like excitatory input circuit formation and hyperexcitation of DGCs. Replenishment of hilar nNOS protein blocked epileptogenic development and memory impairment in pilocarpine-induced TLE mice. Moreover, chronic treatment with DETA/NONOate, a slowly released exogenous nitric oxide (NO) donor, prevented aberrant neural circuits of DGCs and the consequent epileptogenesis without acute antiseizure effects. Therefore, we concluded that NO donor therapy may be a novel anti-epileptogenesis strategy, different from existing antiseizure medications (ASMs), for curing TLE.
海马门区中间神经元变性在颞叶癫痫(TLE)中所起作用的分子机制仍不清楚。特别是,很少有研究关注含神经元型一氧化氮合酶(nNOS,由Nos1编码)的门区中间神经元在TLE中的作用。在本研究中,构建了Nos1条件性敲除小鼠,我们发现选择性敲除门区中间神经元而非齿状颗粒细胞(DGCs)中的Nos1会引发癫痫发生。TLE患者和小鼠中nNOS水平下调。Nos1缺失导致过度的癫痫样兴奋性输入回路形成以及DGCs的过度兴奋。补充门区nNOS蛋白可阻断毛果芸香碱诱导的TLE小鼠的癫痫发生发展和记忆障碍。此外,用缓慢释放的外源性一氧化氮(NO)供体DETA/ NONOate进行长期治疗,可预防DGCs的异常神经回路及随之而来的癫痫发生,且无急性抗癫痫作用。因此,我们得出结论,NO供体疗法可能是一种不同于现有抗癫痫药物(ASMs)的新型抗癫痫发生策略,用于治疗TLE。