Sakhrekar Rajendra, Keane Corinne, Woo Elise, Knapman Myles, McCann Matthew R, Gray Randolph
Department of Spine Surgery, Children Hospital Westmead, Sydney, Australia.
J Orthop Case Rep. 2024 Dec;14(12):202-207. doi: 10.13107/jocr.2024.v14.i12.5074.
Death is the most common outcome of longitudinal atlanto-occipital dissociation (L-AOD). Even though rare, survival is commonly seen in the pediatric population. This study reports a successful outcome of a pediatric patient with an L-AOD without neurodeficits, immobilized in a visor (head-neck-chest) orthosis.
A 9-year-old boy came off his motorbike during a jump at ~50 kph. He was transferred from the primary hospital with spine precautions and a cervical collar with multiple injuries with neurologically intact on presentation. The computed tomography (CT) spine demonstrated a widening of the basion-dens interval, estimated approximately at 16 mm (normal <10 mm), with the widening of the atlanto-occipital articulations with occipital condyles and atlas facet distance markedly widened approximately at 7 mm (normal <5 mm). Considering intact neurology and no complete tear of the tectorial membrane, the decision was made to immobilize in a visor (head-neck-chest) orthosis for controlled vertical cranial settling to occur. Periodic cervical spine imaging over 3 months was done to assess the reduction. At the end of 3 months, dynamic cervical spine X-rays and CT scans confirmed atlanto-occipital articulations with the basion-dens interval and intercondylar distance within normal limits.
L-AOD is a rare diagnosis with a high rate of neurological deficits and mortality. The advancements in emergency care, diagnostic methods, and treatment options have increased survival rates and overall prognosis of the atlanto-occipital dissociation. A visor (head-neck-chest) orthosis and careful observation could be one of the treatment options for L-AOD.
纵向寰枕关节脱位(L-AOD)最常见的结局是死亡。尽管罕见,但小儿患者中常见存活情况。本研究报告了1例无神经功能缺损的小儿L-AOD患者,通过佩戴面罩式(头-颈-胸)矫形器获得成功治疗的病例。
一名9岁男孩在一次约50公里/小时的跳跃中从摩托车上摔下。他从基层医院转运而来,脊柱采取了防护措施,佩戴颈托,多处受伤,就诊时神经功能完好。脊柱计算机断层扫描(CT)显示颅底至齿突间距增宽,估计约为16毫米(正常<10毫米),寰枕关节增宽,枕髁与寰椎小关节面距离明显增宽约7毫米(正常<5毫米)。考虑到神经功能完好且覆膜未完全撕裂,决定佩戴面罩式(头-颈-胸)矫形器固定,以实现可控的垂直颅骨沉降。在3个月内定期进行颈椎成像以评估复位情况。3个月末,颈椎动态X线片和CT扫描证实寰枕关节的颅底至齿突间距和髁间距离在正常范围内。
L-AOD是一种罕见的诊断,神经功能缺损率和死亡率高。急诊护理、诊断方法和治疗选择的进步提高了寰枕关节脱位的生存率和总体预后。面罩式(头-颈-胸)矫形器和仔细观察可能是L-AOD的治疗选择之一。