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与先天性血管异常相关的巨大下腔静脉动脉瘤的手术修复:一例报告

Surgical Repair of a Giant Inferior Vena Cava Aneurysm Associated with a Congenital Vascular Anomaly: A Case Report.

作者信息

Dimitriadis Konstantinos, Papatheodorou Nikolaos, Triantafyllou Nikolaos, Parisidis Stavros, Argyriou Christos, Georgiadis George S

机构信息

Department of Vascular Surgery, University General Hospital of Evros, Democritus University of Thrace, Alexandroupolis, Greece.

Department of Vascular Surgery, University Hospital LMU Munich, Munich, Germany.

出版信息

Vasc Specialist Int. 2024 Dec 18;40:42. doi: 10.5758/vsi.240087.

DOI:10.5758/vsi.240087
PMID:39690709
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11652965/
Abstract

Inferior vena cava aneurysms (IVCAs) are rare yet potentially lethal, especially if they are symptomatic or complicated. Among the IVCAs reported in the literature, only a few are associated with congenital vascular anomalies, including congenital IVC obstruction, tetralogy of Fallot, left-sided IVC, duplicated IVC, Ehlers-Danlos syndrome, blue rubber bleb nevus syndrome, and Klipper-Trenaunay syndrome. We present the case of an 8-cm symptomatic saccular IVCA in a patient with tetralogy of Fallot, treated successfully with surgical repair. Although rare venous pathologies can sometimes be managed with endovascular treatment, open surgical reconstruction remains the mainstay of durable and definitive repair.

摘要

下腔静脉动脉瘤(IVCAs)虽罕见但有潜在致命性,尤其是出现症状或发生并发症时。在文献报道的IVCAs病例中,仅有少数与先天性血管异常相关,包括先天性下腔静脉梗阻、法洛四联症、左侧下腔静脉、重复下腔静脉、埃勒斯-丹洛斯综合征、蓝色橡皮疱痣综合征和克-特综合征。我们报告1例患有法洛四联症的患者,其出现症状的8厘米囊状IVCA经手术修复成功治疗。尽管罕见的静脉病变有时可通过血管内治疗处理,但开放手术重建仍是持久、确定性修复的主要方法。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/4b0966ffc826/vsi-40-42-f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/d987d12749d2/vsi-40-42-f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/44440d8c3475/vsi-40-42-f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/8e20ff2961a0/vsi-40-42-f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/4b0966ffc826/vsi-40-42-f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/d987d12749d2/vsi-40-42-f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/44440d8c3475/vsi-40-42-f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/8e20ff2961a0/vsi-40-42-f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c6d/11652965/4b0966ffc826/vsi-40-42-f4.jpg

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本文引用的文献

1
Endovascular treatment of an inferior vena cava aneurysm in a patient with blue rubber bleb nevus syndrome.蓝色橡皮疱痣综合征患者下腔静脉瘤的血管内治疗。
J Vasc Surg Cases Innov Tech. 2021 Jul 22;7(4):634-635. doi: 10.1016/j.jvscit.2021.07.008. eCollection 2021 Dec.
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Inferior vena cava aneurysm in a patient with Ehlers-Danlos syndrome.一名患有埃勒斯-丹洛斯综合征的患者出现下腔静脉瘤。
J Cardiovasc Comput Tomogr. 2021 Jul-Aug;15(4):e94-e95. doi: 10.1016/j.jcct.2021.03.002. Epub 2021 Mar 13.
3
Balloon angioplasty for symptomatic inferior vena cava aneurysm.
球囊血管成形术治疗症状性下腔静脉动脉瘤。
J Vasc Surg Venous Lymphat Disord. 2018 Sep;6(5):661-663. doi: 10.1016/j.jvsv.2018.04.008. Epub 2018 Jun 15.
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An Inferior Vena Cava Aneurysm in a Patient with Klippel-Trenaunay Syndrome.
Ann Vasc Surg. 2018 Jul;50:300.e1-300.e3. doi: 10.1016/j.avsg.2018.01.092. Epub 2018 Mar 5.
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Endovascular Treatment of a Renocaval Arteriovenous Fistula Induced Inferior Vena Cava Aneurysm.肾腔动静脉瘘致下腔静脉瘤的血管内治疗
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Giant inferior vena cava aneurysm.巨大下腔静脉动脉瘤
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Management of inferior vena cava aneurysm.下腔静脉瘤的管理
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Stent-graft implantation to treat an inferior vena cava aneurysm.支架移植术治疗下腔静脉瘤。
J Endovasc Ther. 2013 Oct;20(5):714-7. doi: 10.1583/13-4368R.1.
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Embolization of a large inferior vena cava aneurysm in a child.
J Vasc Interv Radiol. 2008 Oct;19(10):1509-12. doi: 10.1016/j.jvir.2008.07.012. Epub 2008 Aug 27.
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Aneurysm of the inferior vena cava: case report and review of the literature.下腔静脉动脉瘤:病例报告及文献综述
Phlebology. 2008;23(4):184-8. doi: 10.1258/phleb.2008.008008.