Hibino Makoto, Malas Tarek, Cullen Paul, Gillinov Marc
Department of Thoracic and Cardiovascular Surgery, Heart, Vascular, and Thoracic Institute, Cleveland Clinic, Cleveland, Ohio, USA.
JACC Case Rep. 2024 Nov 20;29(22):102704. doi: 10.1016/j.jaccas.2024.102704.
A 36-year-old man with Marfan syndrome underwent mitral surgery after personalized external aortic root support operation. Redo surgery was performed without aortic cannulation (with right axillary cannulation and retrograde cardioplegia). Surgical findings revealed unique aortic changes with adventitial growth and vasa vasorum, without visible mesh. Further research is crucial to optimize surgical strategies and outcomes.
一名患有马凡综合征的36岁男性在接受个性化体外主动脉根部支撑手术后接受了二尖瓣手术。再次手术时未进行主动脉插管(采用右腋动脉插管和逆行心脏停搏)。手术所见显示主动脉有独特变化,伴有外膜增生和滋养血管,未见明显网状结构。进一步的研究对于优化手术策略和结果至关重要。