Khorsand J, Karakousis C P
Am J Surg. 1985 Feb;149(2):215-8. doi: 10.1016/s0002-9610(85)80067-2.
Nineteen cases of desmoid tumors were reviewed, being intraabdominal. Five of the 7 were associated with polyposis coli. The remaining 12 cases were distributed in different anatomic locations. Sixteen patients were treated with resection either alone or in combination with radiation or hormonal treatment. There were two deaths due to unrelated causes, and the rest of the patients (89 percent) are alive. At present, 16 of the surviving 17 patients are disease-free with a mean follow-up of 6 years. In two of eight patients who were initially treated with wide excision at our center, local recurrence developed, and five patients treated with resection elsewhere were referred because of recurrence. Six patients treated with simple resection and adjuvant radiation remain free of disease with a mean follow-up of 5 1/2 years.
回顾了19例腹内硬纤维瘤病例。7例中有5例与结肠息肉病相关。其余12例分布于不同解剖部位。16例患者接受了单独切除或联合放疗或激素治疗。有2例因无关原因死亡,其余患者(89%)存活。目前,17例存活患者中有16例无疾病,平均随访6年。在我们中心最初接受广泛切除治疗的8例患者中,有2例出现局部复发,另外5例在其他地方接受切除治疗的患者因复发前来就诊。6例接受单纯切除和辅助放疗的患者无疾病复发,平均随访5.5年。