[耳蜗神经缺损儿童的听觉植入问题]
[Issues of auditory implant in children with cochlear nerve deficiency].
作者信息
Zhang Zhihua, Chen Jianqing
机构信息
Department of Otolaryngology Head and Neck Surgery，Ninth Peoples Hospital Affiliated to Shanghai Jiao Tong University School of Medicine，Shanghai，200011，China.
Institute of Otology，School of Medicine，Shanghai Jiao Tong University.
出版信息
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2025 Jan;39(1):7-9. doi: 10.13201/j.issn.2096-7993.2025.01.002.
Abstract
Cochlear nerve deficiency（CND） is a rare inner ear malformation characterized by a hypoplastic or absent cochlear nerve, resulting in variable hearing loss or total deafness, depending on the quantity of nerve fibers present. About 18% of congenital hearing loss are associated with CND. It is a disease of uncertain cause. The outcome of auditory implant in CND patients varies widely. This article will discuss the related issues of CND.
摘要
耳蜗神经缺如（CND）是一种罕见的内耳畸形，其特征为耳蜗神经发育不全或缺失，根据存在的神经纤维数量不同，可导致不同程度的听力损失或全聋。约18%的先天性听力损失与CND有关。这是一种病因不明的疾病。CND患者接受听觉植入的效果差异很大。本文将讨论CND的相关问题。
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本文引用的文献
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A Systematic Review and Meta-analysis Examining Outcomes of Cochlear Implantation in Children With Bilateral Cochlear Nerve Deficiency.双侧耳蜗神经发育不良儿童人工耳蜗植入术后结局的系统评价和荟萃分析
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Diameter of the Cochlear Nerve Canal predicts Cochlear Nerve Deficiency in Children with Sensorineural Hearing Loss.耳蜗神经管直径可预测感音神经性听力损失儿童的耳蜗神经缺失。
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Cochlear Implant Outcomes in Cochlea Nerve Aplasia and Hypoplasia.耳蜗神经发育不全和发育不良患者的人工耳蜗植入效果
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