Zhang Zhihua, Chen Jianqing
Department of Otolaryngology Head and Neck Surgery，Ninth Peoples Hospital Affiliated to Shanghai Jiao Tong University School of Medicine，Shanghai，200011，China.
Institute of Otology，School of Medicine，Shanghai Jiao Tong University.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2025 Jan;39(1):7-9. doi: 10.13201/j.issn.2096-7993.2025.01.002.
Cochlear nerve deficiency（CND） is a rare inner ear malformation characterized by a hypoplastic or absent cochlear nerve, resulting in variable hearing loss or total deafness, depending on the quantity of nerve fibers present. About 18% of congenital hearing loss are associated with CND. It is a disease of uncertain cause. The outcome of auditory implant in CND patients varies widely. This article will discuss the related issues of CND.
耳蜗神经缺如（CND）是一种罕见的内耳畸形，其特征为耳蜗神经发育不全或缺失，根据存在的神经纤维数量不同，可导致不同程度的听力损失或全聋。约18%的先天性听力损失与CND有关。这是一种病因不明的疾病。CND患者接受听觉植入的效果差异很大。本文将讨论CND的相关问题。
