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厄尔德海姆-切斯特病中的反常冠状动脉栓塞:侵入性评估与多学科管理

Paradoxical coronary embolism in Erdheim-Chester disease: invasive assessment and multidisciplinary management.

作者信息

Lamprou Vasileios, Daniels Matthew J, Read Charles D, Keshavarzi Freidoon

机构信息

Manchester Heart Centre, Manchester Royal Infirmary, Oxford Road, Manchester, M13 9WL, United Kingdom.

Faculty of Biology, Medicine and Health, The University of Manchester, Oxford Road, Manchester, M13 9PL, United Kingdom.

出版信息

Oxf Med Case Reports. 2024 Dec 28;2024(12):omae163. doi: 10.1093/omcr/omae163. eCollection 2024 Dec.

DOI:10.1093/omcr/omae163
PMID:39734688
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11682485/
Abstract

We report a case of non-ST elevation myocardial infarction in a 36-year-old man with Erdheim-Chester disease (ECD). Multimodality assessment revealed acute coronary thrombus with simultaneous recurrent pulmonary embolism in spite of compliance with a direct oral anticoagulant. Prior case reports of acute myocardial infarction in this population have not outlined the role of catheter based intravascular assessment and treatment in this rare clinical entity.

摘要

我们报告了一例患有 Erdheim-Chester 病(ECD)的 36 岁男性非 ST 段抬高型心肌梗死病例。多模态评估显示,尽管患者一直服用直接口服抗凝剂,但仍出现急性冠状动脉血栓并同时复发肺栓塞。此前该人群急性心肌梗死的病例报告未阐述基于导管的血管内评估和治疗在这种罕见临床病症中的作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/722163980ae5/omae163f7.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/c2a129be190c/omae163f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/8775fc29edb2/omae163f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/1b56ce25aebd/omae163f5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/2cd010b96a03/omae163f6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/722163980ae5/omae163f7.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/ac460048aea9/omae163f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/c2a129be190c/omae163f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/8775fc29edb2/omae163f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/1b56ce25aebd/omae163f5.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/59ff/11682485/722163980ae5/omae163f7.jpg

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Paradoxical coronary embolism in Erdheim-Chester disease: invasive assessment and multidisciplinary management.厄尔德海姆-切斯特病中的反常冠状动脉栓塞:侵入性评估与多学科管理
Oxf Med Case Reports. 2024 Dec 28;2024(12):omae163. doi: 10.1093/omcr/omae163. eCollection 2024 Dec.
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本文引用的文献

1
Intracoronary Imaging of Coronary Atherosclerotic Plaque: From Assessment of Pathophysiological Mechanisms to Therapeutic Implication.冠状动脉粥样硬化斑块的冠状动脉内影像学:从病理生理机制评估到治疗意义。
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Cardiovascular involvement in Erdheim-Chester diseases is associated with myocardial fibrosis and atrial dysfunction. Erdheim-Chester 病的心血管受累与心肌纤维化和心房功能障碍有关。
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Erdheim-Chester disease: consensus recommendations for evaluation, diagnosis, and treatment in the molecular era.骨硬化性嗜酸性肉芽肿:分子时代下的评估、诊断和治疗的共识建议。
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Coronary Embolus: An Underappreciated Cause of Acute Coronary Syndromes.冠状动脉栓子:急性冠状动脉综合征的一个被低估的病因。
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Cardiovascular manifestations of Erdheim-Chester disease.厄尔德海姆-切斯特病的心血管表现
Clin Exp Rheumatol. 2015 Mar-Apr;33(2 Suppl 89):S-155-63. Epub 2015 Feb 18.
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Erdheim-Chester disease: CT findings of thoracic involvement.厄尔-道伊姆-切斯特病:胸部受累的 CT 表现。
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Multimodality imaging showing complete cardiovascular involvement by Erdheim-Chester disease.多模态成像显示埃尔迪希姆-切斯特病累及整个心血管系统。
Eur J Echocardiogr. 2010 Aug;11(7):E25. doi: 10.1093/ejechocard/jeq052. Epub 2010 Apr 20.
10
Cardiovascular involvement, an overlooked feature of Erdheim-Chester disease: report of 6 new cases and a literature review.心血管受累:一种被忽视的 Erdheim-Chester 病特征——6 例新病例报告及文献综述
Medicine (Baltimore). 2004 Nov;83(6):371-392. doi: 10.1097/01.md.0000145368.17934.91.