Flourou Christina, Azina Chara, Georgiou George, Anastasiadou Violetta
Department of Internal Medicine, Nicosia General Hospital, Nicosia, CYP.
Department of Histopathology, Nicosia General Hospital, Nicosia, CYP.
Cureus. 2025 Jan 8;17(1):e77146. doi: 10.7759/cureus.77146. eCollection 2025 Jan.
Metabolic-dysfunction-associated steatotic liver disease (MASLD) is the most common chronic liver disease in the Western world. MASLD-associated cirrhosis prevalence is on the rise along with the obesity and metabolic syndrome epidemic. Genetic factors are included in the multi-hit model of MASLD pathogenesis and insulin-like growth factor-1 (IGF-1) has an important role. We report the case of a man who was referred to a hepatology clinic due to elevated liver enzymes as probable drug-induced liver injury (DILI). A 35-year-old man was diagnosed with compensated cirrhosis with an estimated Child-Pugh score of 5 points (Class A) and underwent further investigation of the causative factor. MASLD-cirrhosis was the preliminary diagnosis, but high serum and urine copper levels needed further investigation. Whole-genome sequencing revealed heterozygosity for a rare variant of the IGF-1 receptor, a metabolic factor whose role is crucial in the GH/IGF-1 axis to fatty liver and cirrhosis. MASLD diagnosis is really challenging, especially at the progressive stages of fibrosis. Clinical features, somatometric parameters, laboratory tests and liver biopsy guide us to establish the diagnosis. Despite all these findings, the heterogeneity of disease's pathogenesis through metabolic pathways underlines the need for deeper investigation, especially genetic factors such as IGF-1 and their penetration in disease progression and liver fibrosis.
代谢功能障碍相关脂肪性肝病(MASLD)是西方世界最常见的慢性肝病。随着肥胖和代谢综合征的流行,MASLD相关肝硬化的患病率正在上升。遗传因素包含在MASLD发病机制的多因素模型中,胰岛素样生长因子-1(IGF-1)起着重要作用。我们报告了一例因肝酶升高被转诊至肝病诊所,疑似药物性肝损伤(DILI)的男性病例。一名35岁男性被诊断为代偿期肝硬化,估计Child-Pugh评分为5分(A级),并对病因进行了进一步调查。初步诊断为MASLD肝硬化,但血清和尿铜水平升高需要进一步调查。全基因组测序显示IGF-1受体的一种罕见变异存在杂合性,IGF-1是一种代谢因子,在生长激素/IGF-1轴对脂肪肝和肝硬化的作用中至关重要。MASLD的诊断极具挑战性,尤其是在纤维化的进展阶段。临床特征、人体测量参数、实验室检查和肝活检指导我们进行诊断。尽管有所有这些发现,但疾病通过代谢途径发病机制的异质性强调了深入研究的必要性,特别是像IGF-1这样的遗传因素及其在疾病进展和肝纤维化中的作用。