Ma Dan, Wei Junlin, He Honghui, Yang Wenjun, Mo Zhaohui, Wang Fang
Department of Endocrinology, Third Xiangya Hospital, Central South University, Changsha 410013, China.
Zhong Nan Da Xue Xue Bao Yi Xue Ban. 2024 Jul 28;49(7):1073-1081. doi: 10.11817/j.issn.1672-7347.2024.240421.
IgG4-related disease (IgG4-RD) is an immune-mediated fibroinflammatory disorder that can affect multiple organs throughout the body, predominantly in middle-aged and elderly males, with a male-to-female ratio of 2꞉1 to 3꞉1. IgG4-related retroperitoneal fibrosis (IgG4-RPF), a rare subtype of IgG4-RD, has an unclear etiology, and its comorbidity with type 2 diabetes mellitus is also uncommon. A lack of awareness of this condition in clinical practice can easily lead to misdiagnosis. On July 14, 2016, the Third Xiangya Hospital of Central South University admitted a patient with type 2 diabetes mellitus complicated by IgG4-RPF. Following comprehensive treatment, including blood glucose and blood pressure control, kidney protection, circulation improvement, and the use of prednisone, the patient's condition significantly improved. The retroperitoneal fibrotic mass decreased in size, renal function improved, and serum IgG4 levels decreased. After 8 years of follow-up, the condition did not recur. Analyzing this case in conjunction with a literature review suggests that the development of IgG4-RPF in diabetic patients may be related to chronic inflammation from metabolic syndrome and atherosclerotic plaques associated with long-standing diabetes. This provides valuable clinical ideas for clinicians in diagnosing and treating this rare comorbidity.
IgG4相关疾病(IgG4-RD)是一种免疫介导的纤维炎症性疾病,可累及全身多个器官,主要发生于中老年男性,男女比例为2∶1至3∶1。IgG4相关腹膜后纤维化(IgG4-RPF)是IgG4-RD的一种罕见亚型,病因不明,与2型糖尿病的合并症也不常见。临床实践中对这种疾病认识不足容易导致误诊。2016年7月14日,中南大学湘雅三医院收治了一名合并IgG4-RPF的2型糖尿病患者。经过综合治疗,包括控制血糖和血压、保护肾脏、改善循环以及使用泼尼松,患者病情明显改善。腹膜后纤维化肿块缩小,肾功能改善,血清IgG4水平下降。经过8年随访,病情未复发。结合文献复习分析该病例表明,糖尿病患者IgG4-RPF的发生可能与代谢综合征引起的慢性炎症以及长期糖尿病相关的动脉粥样硬化斑块有关。这为临床医生诊断和治疗这种罕见的合并症提供了有价值的临床思路。