• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利：CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法，用中文像聊天一样搜索，搜遍4000万医学文献。AI智能推荐，让科研检索更轻松。

立即免费搜索

文件翻译

保留排版，准确专业，支持PDF/Word/PPT等文件格式，支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述，25分钟生成高质量综述，智能提取关键信息，辅助科研写作。

立即免费体验

1岁患有PHACE综合征女童迂曲性主动脉弓远端动脉瘤的修复

Repair of Tortuous Distal Aortic Arch Aneurysm in a 1-Year-Old Girl With PHACE Syndrome.

作者信息

Okamoto Koji, Ochiai Yoshie, Joo Kunihiko, Yamashita Yoshiyuki, Nakata Yusuke, Muneuchi Jun, Tokunaga Shigehiko

机构信息

Department of Cardiovascular Surgery, Japan Community Healthcare Organization (JCHO) Kyushu Hospital, Kitakyushu-city, Japan.

Department of Pediatric Cardiology, Japan Community Healthcare Organization (JCHO) Kyushu Hospital, Kitakyushu-city, Japan.

出版信息

Ann Thorac Surg Short Rep. 2023 Feb 20;1(2):325-327. doi: 10.1016/j.atssr.2023.02.004. eCollection 2023 Jun.

DOI:10.1016/j.atssr.2023.02.004
PMID:39790337
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11708387/
Abstract

Herein, we describe a 21-month-old girl with PHACE syndrome (posterior fossa hemangiomas, arterial lesions, cardiac anomalies/coarctation of the aorta, and eye anomalies) who presented with a tortuous extensive aortic arch aneurysm. As the maximum short diameter of the distal aortic arch aneurysm expanded rapidly from 21 mm to 25 mm in only 5 months, we performed extensive aortic arch reconstruction with interposition graft replacement through a left thoracotomy under partial cardiopulmonary bypass.

摘要

在此，我们描述了一名患有PHACE综合征（后颅窝血管瘤、动脉病变、心脏异常/主动脉缩窄以及眼部异常）的21个月大女童，她出现了一个迂曲的广泛性主动脉弓动脉瘤。由于仅在5个月内，远端主动脉弓动脉瘤的最大短径就从21毫米迅速扩大到25毫米，我们在部分体外循环下通过左胸切口进行了带血管移植的广泛性主动脉弓重建术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/27fd643f4c61/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/d55331903c78/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/65f0d66392e0/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/27fd643f4c61/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/d55331903c78/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/65f0d66392e0/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e9bd/11708387/27fd643f4c61/gr3.jpg

相似文献

1
Repair of Tortuous Distal Aortic Arch Aneurysm in a 1-Year-Old Girl With PHACE Syndrome.1岁患有PHACE综合征女童迂曲性主动脉弓远端动脉瘤的修复
Ann Thorac Surg Short Rep. 2023 Feb 20;1(2):325-327. doi: 10.1016/j.atssr.2023.02.004. eCollection 2023 Jun.
2
A rare combination of post-ductal coarctation of the aorta and adjunct tortuous aneurysm: a neonate with Posterior fossa anomalies, Haemangiomas of the head and neck, Arterial, Cardiovascular, and Eye anomalies and ventral developmental defect syndrome.一种罕见的主动脉导管后缩窄合并附属迂曲型动脉瘤：一种后颅窝畸形、头颈部血管瘤、动脉、心血管和眼部异常及腹侧发育缺陷综合征的新生儿。
Cardiol Young. 2022 Aug;32(8):1360-1362. doi: 10.1017/S1047951121005102. Epub 2022 Jan 6.
3
Ipsilateral hemangioma and aortic arch anomalies in posterior fossa malformations, hemangiomas, arterial anomalies, coarctation of the aorta, and cardiac defects and eye abnormalities (PHACE) anomaly: report and review.后颅窝畸形、血管瘤、动脉异常、主动脉缩窄、心脏缺陷和眼部异常（PHACE）综合征中的同侧血管瘤与主动脉弓异常：病例报告及文献复习
Pediatrics. 2004 Feb;113(2):412-5. doi: 10.1542/peds.113.2.412.
4
PHACE(S) syndrome: Report of a case with new ocular and systemic manifestations.PHACE(S)综合征：1例伴有新的眼部和全身表现的病例报告。
J Curr Ophthalmol. 2016 Dec 27;29(2):136-138. doi: 10.1016/j.joco.2016.10.005. eCollection 2017 Jun.
5
Aortic arch repair in children with PHACE syndrome.儿童肺动脉高压合并额面血管瘤综合征的主动脉弓修复。
J Thorac Cardiovasc Surg. 2016 Sep;152(3):709-17. doi: 10.1016/j.jtcvs.2016.03.082. Epub 2016 Apr 14.
6
Surgical repair of interrupted right-sided cervical aortic arch with hypoplasia of the descending thoracic aorta in a child with PHACE syndrome.患儿患有 PHACE 综合征，伴右侧颈总动脉弓中断及降主动脉发育不良，行外科修复。
Eur J Cardiothorac Surg. 2023 May 2;63(5). doi: 10.1093/ejcts/ezad171.
7
Anomaly of Haughton type D left cervical aortic arch in combination with type B dissection: case report and literature review.哈顿D型左颈主动脉弓异常合并B型夹层：病例报告及文献综述
J Cardiothorac Surg. 2018 Jun 27;13(1):79. doi: 10.1186/s13019-018-0768-8.
8
Stroke in children with posterior fossa brain malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities (PHACE) syndrome: a systematic review of the literature.儿童后颅窝脑畸形、血管瘤、动脉异常、主动脉缩窄和心脏缺损以及眼部异常（PHACE）综合征中的脑卒中：文献系统评价。
Stroke. 2012 Jun;43(6):1672-4. doi: 10.1161/STROKEAHA.112.650952. Epub 2012 Mar 22.
9
Aortic arch tortuosity with PHACE syndrome - a rare case scenario.主动脉弓迂曲合并PHACE综合征——一种罕见病例情况。
Images Paediatr Cardiol. 2016 Apr-Jun;18(2):1-4.
10
Progress in the treatment of aneurysms of the distal aortic arch: approach through median sternotomy.远端主动脉弓动脉瘤治疗进展：经正中胸骨切开术入路
J Cardiovasc Surg (Torino). 2003 Apr;44(2):243-8.

本文引用的文献

1
Aortic arch anomalies in PHACE syndrome: An individualized approach to an unusual problem.PHACE综合征中的主动脉弓异常：针对一个特殊问题的个体化方法。
J Thorac Cardiovasc Surg. 2016 Sep;152(3):718-9. doi: 10.1016/j.jtcvs.2016.04.039. Epub 2016 Apr 19.
2
Aortic arch repair in children with PHACE syndrome.儿童肺动脉高压合并额面血管瘤综合征的主动脉弓修复。
J Thorac Cardiovasc Surg. 2016 Sep;152(3):709-17. doi: 10.1016/j.jtcvs.2016.03.082. Epub 2016 Apr 14.
3
Congenital cardiac, aortic arch, and vascular bed anomalies in PHACE syndrome (from the International PHACE Syndrome Registry).
PHACE 综合征中的先天性心脏、主动脉弓和血管床异常（来自国际 PHACE 综合征登记处）。
Am J Cardiol. 2013 Dec 15;112(12):1948-52. doi: 10.1016/j.amjcard.2013.08.025. Epub 2013 Sep 28.
4
Selective use of left heart bypass for aortic coarctation.选择性使用左心旁路术治疗主动脉缩窄。
Ann Thorac Surg. 2010 Mar;89(3):851-6; discussion 856-7. doi: 10.1016/j.athoracsur.2009.11.060.
5
Consensus Statement on Diagnostic Criteria for PHACE Syndrome.PHACE综合征诊断标准共识声明。
Pediatrics. 2009 Nov;124(5):1447-56. doi: 10.1542/peds.2009-0082. Epub 2009 Oct 26.
6
Use of partial cardiopulmonary bypass for coarctation repair through a left thoracotomy in children without collaterals.在无侧支循环的儿童中，通过左胸切口采用部分体外循环进行缩窄修复。
Ann Thorac Surg. 2006 Sep;82(3):964-72. doi: 10.1016/j.athoracsur.2006.04.060.
7
Repair of a complex aortic arch anomaly associated with cutaneous hemangioma.与皮肤血管瘤相关的复杂主动脉弓畸形修复术。
Ann Thorac Surg. 2002 Jul;74(1):245-6. doi: 10.1016/s0003-4975(02)03554-3.