Kang Lillian, Hoover Anna C, Camitta Michael, Turek Joseph W, Andersen Nicholas D
Department of Surgery, Duke University Medical Center, Durham, North Carolina.
Duke University Medical School, Durham, North Carolina.
Ann Thorac Surg Short Rep. 2023 Jun 10;1(3):444-446. doi: 10.1016/j.atssr.2023.05.015. eCollection 2023 Sep.
Congenital Gerbode defects, consisting of a deficiency in the membranous septum causing left ventricle-to-right atrium shunting, are rarely hemodynamically significant. Here, we present the case of a neonate with a large unrestrictive Gerbode defect, patent foramen ovale, patent ductus arteriosus, and pulmonary valve insufficiency resulting in a circular intracardiac shunt and cardiogenic shock. The patient was managed with venoarterial extracorporeal membrane oxygenation followed by neonatal Gerbode defect repair. After repair, the patient had an uncomplicated postoperative course. To our knowledge, a neonatal congenital Gerbode defect resulting in cardiogenic shock is exceedingly rare.
先天性Gerbode缺损是指膜性间隔缺损导致左心室向右心房分流,很少具有血流动力学意义。在此,我们报告一例患有巨大非限制性Gerbode缺损、卵圆孔未闭、动脉导管未闭和肺动脉瓣关闭不全的新生儿病例,该病例导致心内循环分流和心源性休克。该患者接受了静脉-动脉体外膜肺氧合治疗,随后进行了新生儿Gerbode缺损修复术。修复术后,患者术后恢复过程顺利。据我们所知,新生儿先天性Gerbode缺损导致心源性休克极为罕见。