M Jaiganesh, Mishra Kirtisudha, Sharma Shikha, Kumar Manish, Patel Ankita
Department of Pediatrics, Chacha Nehru Bal Chikitsalaya, Delhi, 110031, India.
Department of Biochemistry, Chacha Nehru Bal Chikitsalaya, Delhi, India.
Pediatr Nephrol. 2025 May;40(5):1645-1651. doi: 10.1007/s00467-024-06645-6. Epub 2025 Jan 10.
Hypothalamic-pituitary-adrenal (HPA) axis recovery after cessation of steroid therapy in children with nephrotic syndrome (NS) has hardly been studied in the literature.
This 22-month cross-sectional study recruited children (2-14 years) with NS, having received a minimum 3 months of prednisolone, now in remission, and off steroids for 1, 3, or 6 months. Serum cortisol-basal and stimulated (with long-acting intramuscular adrenocorticotropic hormone), and factors affecting them, were assessed. Low basal and stimulated cortisol were taken as < 138 nmol/L and < 500 nmol/L, respectively.
Of 80 (60 males) children, median (IQR) age 64 (43, 91.7) months, most were infrequently relapsing (34; 42.5%) or had a single episode of NS (35; 43.8%). As per duration since discontinuation, 23 (28.8%), 35 (43.8%), and 22 (27.4%) children were off steroids for 1, 3, and 6 months, respectively. Overall, 8 (10%) and 26 (32.5%) had low basal and stimulated cortisol levels, respectively. Proportions of children with HPA axis suppression (low peak cortisol) were 9/23 (39%), 12/35 (34%), and 5/22 (23%) in the groups off steroids for 1, 3, and 6 months, respectively. Optimal peak cortisol level, indicating adrenal recovery, was independently associated with duration since cessation of prednisolone [odds ratio (6 months vs. 1 month) was 10.07 (95%CI 1.46 to 69.51); P = 0.019] and basal cortisol levels > 138 nmol/L (odds ratio 25.0 (95%CI 2.94 to 200); P = 0.03).
Nearly two-thirds of children with mild courses of NS demonstrate optimal HPA axis function between 1 and 6 months post cessation of steroids. Duration since cessation and basal cortisol independently predict optimal adrenal response.
关于肾病综合征(NS)患儿停用类固醇治疗后下丘脑 - 垂体 - 肾上腺(HPA)轴的恢复情况,在文献中几乎没有相关研究。
这项为期22个月的横断面研究招募了年龄在2至14岁的NS患儿,这些患儿至少接受了3个月的泼尼松龙治疗,目前处于缓解期,且已停用类固醇1、3或6个月。评估了血清基础皮质醇和刺激后皮质醇(使用长效肌肉注射促肾上腺皮质激素)以及影响它们的因素。基础皮质醇和刺激后皮质醇水平低分别定义为<138 nmol/L和<500 nmol/L。
80名(60名男性)患儿,中位(四分位间距)年龄64(43,91.7)个月,大多数患儿复发不频繁(34例;42.5%)或仅有一次NS发作(35例;43.8%)。根据停药后的持续时间,分别有23例(28.8%)、35例(43.8%)和22例(27.4%)患儿停用类固醇1、3和6个月。总体而言,分别有8例(10%)和26例(32.5%)患儿基础皮质醇和刺激后皮质醇水平低。在停用类固醇1、3和6个月的组中,HPA轴抑制(皮质醇峰值低)的患儿比例分别为9/23(39%)、12/35(34%)和5/22(23%)。表明肾上腺恢复的最佳皮质醇峰值水平与停用泼尼松龙后的持续时间独立相关[比值比(6个月对1个月)为10.07(95%置信区间1.46至69.51);P = 0.019],且基础皮质醇水平>138 nmol/L(比值比25.0(95%置信区间2.94至200);P = 0.03)。
近三分之二病程较轻的NS患儿在停用类固醇后1至6个月内显示出最佳的HPA轴功能。停药后的持续时间和基础皮质醇可独立预测肾上腺的最佳反应。