Chen Joanna, Bautista Catherine H, Patel Ashraf, French Mackenzie M, Mienko Anna, Schaeffer Anthony J, Wallis M Chad, Gociman Barbu
From the Division of Plastic and Reconstructive Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, UT.
Department of Surgery, New York Institute of Technology College of Osteopathic Medicine, Long Island, NY.
Plast Reconstr Surg Glob Open. 2025 Jan 10;13(1):e6412. doi: 10.1097/GOX.0000000000006412. eCollection 2025 Jan.
Aphallia is an exceedingly rare congenital malformation. The condition is the result of a sporadic anatomic anomaly during fetal development in a 46, XY male patient with otherwise normal functioning testes and male sexual hormone metabolism. Neophallus reconstruction using the De Castro phalloplasty technique is currently the most accepted treatment modality for this condition. However, most case reports in the literature do not use tissue expansion. To achieve a larger neophallus and possibly decrease the need for secondary phalloplasty postpuberty, tissue expansion should be a standardized adjunct to the De Castro procedure in the management of all patients with congenital aphallia.
无阴茎畸形是一种极其罕见的先天性畸形。这种情况是由于一名46, XY男性患者在胎儿发育期间出现散发性解剖异常所致,其睾丸功能和男性性激素代谢正常。目前,使用德卡斯特罗阴茎成形术技术进行新阴茎重建是治疗这种疾病最被认可的治疗方式。然而,文献中的大多数病例报告并未使用组织扩张术。为了获得更大的新阴茎,并可能减少青春期后二次阴茎成形术的需求,在所有先天性无阴茎畸形患者的治疗中,组织扩张术应作为德卡斯特罗手术的标准化辅助手段。