Ye Zixing, Ou Minjie, Zhang Yushi, Wen Jin
Department of Urology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing, China.
Gland Surg. 2024 Dec 31;13(12):2430-2437. doi: 10.21037/gs-24-371. Epub 2024 Dec 27.
Pheochromocytoma is a rare neuroendocrine tumor, and bilateral pheochromocytomas is even less common. Due to the limited experience with such cases, this study aims to explore the optimal surgical strategy, assess the potential advantages of robotic surgery, and evaluate surgical outcomes for managing bilateral pheochromocytomas.
This report presented a case of a 33-year-old woman with bilateral pheochromocytomas related to multiple endocrine neoplasia type 2a (MEN2A), who was successfully managed by synchronous transperitoneal robotic-assisted bilateral cortical-sparing adrenalectomy. This strategy reduced blood loss, improved cosmetic outcomes, preserved adrenal function, and gradually reduced the need for hormone replacement, ultimately leading to discontinuation of hydrocortisone therapy. The surgery was performed without significant complications. The patient recovered well and had normal blood pressure and hormone level at the 1-year postoperative follow-up.
Synchronous transperitoneal robotic-assisted bilateral cortical-sparing adrenalectomy is a safe, effective, and efficient approach for bilateral pheochromocytomas, and is favorable for rapid recovery and cosmetic demand. This treatment is more advantageous when dealing with multiple neuroendocrine tumors.
嗜铬细胞瘤是一种罕见的神经内分泌肿瘤，双侧嗜铬细胞瘤更为少见。由于此类病例经验有限，本研究旨在探索最佳手术策略，评估机器人手术的潜在优势，并评估双侧嗜铬细胞瘤的手术效果。
本报告介绍了一例33岁患有与2a型多发性内分泌肿瘤（MEN2A）相关的双侧嗜铬细胞瘤的女性患者，她通过同步经腹机器人辅助双侧保留肾上腺皮质切除术成功治疗。该策略减少了失血，改善了美容效果，保留了肾上腺功能，并逐渐减少了激素替代的需求，最终停止了氢化可的松治疗。手术无明显并发症。患者恢复良好，术后1年随访时血压和激素水平正常。
同步经腹机器人辅助双侧保留肾上腺皮质切除术是治疗双侧嗜铬细胞瘤的一种安全、有效且高效的方法，有利于快速康复和满足美容需求。在处理多发性神经内分泌肿瘤时，这种治疗方法更具优势。
