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腹腔镜子宫切除术后播散性腹膜平滑肌瘤病的罕见表现及其多学科管理

A Rare Presentation of Disseminated Peritoneal Leiomyomatosis Following Laparoscopic Hysterectomy and Its Multidisciplinary Management.

作者信息

Balaji Adhithya N, Balasubramanian Balaji, Arora Simran, Shetty Panna

机构信息

Internal Medicine, Università Cattolica Del Sacro Cuore, Rome, ITA.

Surgery and Oncology, New Medical Centre Specialty Hospital, Abu Dhabi, ARE.

出版信息

Cureus. 2024 Dec 16;16(12):e75829. doi: 10.7759/cureus.75829. eCollection 2024 Dec.

DOI:10.7759/cureus.75829
PMID:39822433
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11738093/
Abstract

Disseminated peritoneal leiomyomatosis (DPL) is a rare entity. It is a benign disease but can mimic disseminated malignancy with extensive disease at multiple sites within the abdominopelvic cavity. The primary contributing factor is postulated to be peritoneal spillage of benign leiomyoma, especially after laparoscopic intervention, although hormonal influences might also play a role. It primarily affects females of childbearing age. Cross-sectional imaging studies offer guidance regarding the extensive nature of the disease and surgery is the primary treatment modality. Complete resection, personalized according to the extent of the disease, has to be planned through a multidisciplinary approach. The diagnosis can only be confirmed by histopathology. Hormone suppression might have a role in selected cases.

摘要

播散性腹膜平滑肌瘤病(DPL)是一种罕见疾病。它是一种良性疾病,但可在腹腔盆腔内多个部位出现广泛病变,类似播散性恶性肿瘤。据推测,主要促成因素是良性平滑肌瘤的腹膜播散,尤其是在腹腔镜干预后,不过激素影响可能也起作用。它主要影响育龄女性。横断面成像研究可为疾病的广泛程度提供指导,手术是主要治疗方式。必须通过多学科方法,根据疾病范围规划个体化的完整切除。诊断只能通过组织病理学确诊。在特定病例中,激素抑制可能起作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/f0800f36c9b6/cureus-0016-00000075829-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/a8ee08272892/cureus-0016-00000075829-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/8a1ded73da42/cureus-0016-00000075829-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/f0800f36c9b6/cureus-0016-00000075829-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/a8ee08272892/cureus-0016-00000075829-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/8a1ded73da42/cureus-0016-00000075829-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab04/11738093/f0800f36c9b6/cureus-0016-00000075829-i03.jpg

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本文引用的文献

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Disseminated peritoneal leiomyomatosis: A benign condition with diagnostic and therapeutic challenges.播散性腹膜平滑肌瘤病:一种具有诊断和治疗挑战的良性疾病。
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Disseminated Peritoneal Leiomyomatosis-A Challenging Diagnosis-Mimicking Malignancy Scoping Review of the Last 14 Years.播散性腹膜平滑肌瘤病——一项具有挑战性的诊断——过去14年模仿恶性肿瘤的范围综述
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A Case of Cotyledonoid Dissecting Leiomyoma With Associated Disseminated Peritoneal Leiomyomatosis: The Significance of Frozen Section in Identification of This Unusual Entity.
1例伴有播散性腹膜平滑肌瘤病的叶状分割性平滑肌瘤病例:冰冻切片在识别这一罕见实体中的意义
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Radiol Case Rep. 2023 Apr 14;18(6):2237-2240. doi: 10.1016/j.radcr.2023.03.022. eCollection 2023 Jun.
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Iatrogenic Parasitic Leiomyomas: A Late and Uncommon Complication After Laparoscopic Morcellation.医源性寄生性平滑肌瘤:腹腔镜碎瘤术后一种罕见的晚期并发症
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Front Surg. 2021 Dec 9;8:788749. doi: 10.3389/fsurg.2021.788749. eCollection 2021.
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J Int Med Res. 2021 Aug;49(8):3000605211033194. doi: 10.1177/03000605211033194.
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