Celayir Arın, Deniz Yahya, Ozer Mete, Ozsahin Mahmut K, Botanlioglu Huseyin
Department of Orthopaedics and Traumatology, Cerrahpasa Faculty of Medicine, Istanbul University - Cerrahpasa, Istanbul, TUR.
Cureus. 2024 Dec 17;16(12):e75848. doi: 10.7759/cureus.75848. eCollection 2024 Dec.
Extraskeletal Ewing sarcoma (EES) is a rare and aggressive malignancy originating in soft tissues, distinct from osseous Ewing sarcoma. It commonly affects adolescents and young adults but can occur at any age. Due to its rarity and overlapping clinical features with other malignancies, EES poses significant diagnostic and therapeutic challenges. Accurate diagnosis requires a multidisciplinary approach, incorporating imaging, histopathological evaluation, and molecular testing, such as the detection of the EWSR1-FLI1 fusion protein. This case series highlights two instances of EES involving the scapular and arm regions. The clinical presentations, diagnostic workup, and management strategies, including surgery, chemotherapy, and radiotherapy, are detailed. These cases underscore the importance of a collaborative and individualized approach to managing EES. They also contribute valuable insights to the understanding and treatment of this rare malignancy, emphasizing the need for ongoing research and multidisciplinary collaboration in achieving optimal outcomes.
骨外尤文肉瘤(EES)是一种起源于软组织的罕见侵袭性恶性肿瘤,与骨尤文肉瘤不同。它通常影响青少年和年轻人,但可发生于任何年龄。由于其罕见性以及与其他恶性肿瘤重叠的临床特征,EES带来了重大的诊断和治疗挑战。准确诊断需要多学科方法,包括影像学检查、组织病理学评估和分子检测,如检测EWSR1-FLI1融合蛋白。本病例系列突出了两例累及肩胛骨和手臂区域的EES。详细介绍了临床表现、诊断检查以及包括手术、化疗和放疗在内的管理策略。这些病例强调了采用协作性和个体化方法管理EES的重要性。它们还为理解和治疗这种罕见恶性肿瘤提供了宝贵见解,强调了在实现最佳治疗效果方面持续研究和多学科协作的必要性。