Kudsi Maysoun, Tarcha Raghad, Khalayli Naram, Rabah Nour, Rabah Karam, Alghawe Fatima Alzahraa
Professor of Rheumatology, Faculty of Medicine, Damascus University, Damascus, Syria.
Department of Rheumatology, Faculty of Medicine, Damascus University, Damascus, Syria.
Oxf Med Case Reports. 2025 Jan 18;2025(1):omae179. doi: 10.1093/omcr/omae179. eCollection 2025 Jan.
IgG4-related disease (IgG4-RD) is a rare but increasingly recognised condition that can involve multiple organs, including the kidneys which often presents as tubulointerstitial nephritis. Treatment with glucocorticoids is the first line of therapy, but other options may be needed in refractory cases. This case report explores a 68-year-old female, diagnosed with the patient initially responded to glucocorticoids but had a relapse, leading to progressive renal insufficiency and ultimately death. Our case is a rare case observing the progression to end-stage kidney disease from IgG4-RD, and the first case of which the patient had died in a short period.
IgG4相关疾病(IgG4-RD)是一种罕见但越来越受到认可的疾病,可累及多个器官,包括肾脏,肾脏受累时通常表现为肾小管间质性肾炎。糖皮质激素治疗是一线治疗方法,但难治性病例可能需要其他治疗选择。本病例报告探讨了一名68岁女性,该患者最初对糖皮质激素治疗有反应,但病情复发,导致进行性肾功能不全并最终死亡。我们的病例是观察到IgG4-RD进展为终末期肾病的罕见病例,也是首例患者在短期内死亡的病例。