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一名32岁孕妇的特发性声门下狭窄。

Idiopathic subglottic stenosis in a 32-year-old pregnant woman.

作者信息

Toennesen Bo, Kjærgaard Thomas, Schmid Johannes Martin

机构信息

Department of Clinical Medicine, Aarhus University & Department of Respiratory Diseases and Allergy, Aarhus University Hospital, Aarhus, Denmark.

Department of Oto-Rhino-laryngology, Head and Neck Surgery Aarhus University Hospital, Aarhus, Denmark.

出版信息

Eur Clin Respir J. 2025 Jan 24;12(1):2456312. doi: 10.1080/20018525.2025.2456312. eCollection 2025.

DOI:10.1080/20018525.2025.2456312
PMID:39872798
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11770863/
Abstract

Diagnosis of subglottic stenosis remains greatly a challenge for physicians due to case rarity and presentation of symptoms imitating several other more prevalent medical disorders. Idiopathic subglottic stenosis most often occurs in previously healthy perimenopausal Caucasian women. Several cases have reported symptom progression and increased stenosis, during or in between pregnancies in younger women. The following case of a 32-year-old woman provides an example of significantly long duration from initial symptom onset to diagnosis of idiopathic subglottic stenosis. Additionally, the case illustrates how pregnancy complicates diagnosis and due to the potential risk of stenosis progression and complications during labour, the patient had to undergo surgery with balloon-dilation at week 17 of pregnancy.

摘要

由于病例罕见且症状表现类似其他几种更常见的医学病症,声门下狭窄的诊断对医生来说仍然是一个巨大的挑战。特发性声门下狭窄最常发生在既往健康的围绝经期白人女性中。有几例报告称,年轻女性在孕期或两次妊娠之间症状进展且狭窄加重。以下这位32岁女性的病例说明了从最初症状出现到特发性声门下狭窄诊断之间的显著长时间间隔。此外,该病例还说明了妊娠如何使诊断复杂化,并且由于分娩期间狭窄进展和并发症的潜在风险,患者不得不在妊娠第17周接受球囊扩张手术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/24c542fe36cf/ZECR_A_2456312_F0004_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/74ae3196a287/ZECR_A_2456312_F0001_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/4571ea522e97/ZECR_A_2456312_F0002_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/d8471b7508fc/ZECR_A_2456312_F0003_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/24c542fe36cf/ZECR_A_2456312_F0004_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/74ae3196a287/ZECR_A_2456312_F0001_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/4571ea522e97/ZECR_A_2456312_F0002_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/d8471b7508fc/ZECR_A_2456312_F0003_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3129/11770863/24c542fe36cf/ZECR_A_2456312_F0004_OC.jpg

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本文引用的文献

1
Challenges and successful management of subglottic tracheal stenosis in a 2‑year‑old child: A case report and a mini‑review of the literature.一名2岁儿童声门下气管狭窄的挑战与成功管理:病例报告及文献综述
Med Int (Lond). 2023 Sep 20;3(5):53. doi: 10.3892/mi.2023.113. eCollection 2023 Sep-Oct.
2
Localizing Hormone Receptor Expression to Cellular Compartments in Idiopathic Subglottic Stenosis.特发性声门下狭窄中激素受体表达的细胞区室定位。
Laryngoscope. 2023 Dec;133(12):3506-3511. doi: 10.1002/lary.30856. Epub 2023 Jun 29.
3
Subglottic tracheal stenosis complicating pregnancy: A case report.
妊娠合并声门下气管狭窄:一例报告
Obstet Med. 2022 Sep;15(3):205-207. doi: 10.1177/1753495X21990220. Epub 2021 Feb 10.
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Molecular Mechanisms and Physiological Changes behind Benign Tracheal and Subglottic Stenosis in Adults.成人良性气管和会厌下狭窄的分子机制和生理变化。
Int J Mol Sci. 2022 Feb 22;23(5):2421. doi: 10.3390/ijms23052421.
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An Updated Review of Subglottic Stenosis: Etiology, Evaluation, and Management.声门下狭窄的最新综述:病因、评估与管理
Curr Pulmonol Rep. 2022;11(2):29-38. doi: 10.1007/s13665-022-00286-6. Epub 2022 Mar 3.
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Idiopathic subglottic stenosis and the consequences in cardiopulmonary exercise testing.特发性声门下狭窄及心肺运动试验的后果。
BMJ Case Rep. 2021 Nov 30;14(11):e242149. doi: 10.1136/bcr-2021-242149.
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Delayed Diagnosis of Idiopathic Subglottic Stenosis.特发性声门下狭窄的延误诊断。
Laryngoscope. 2022 Feb;132(2):413-418. doi: 10.1002/lary.29783. Epub 2021 Aug 9.
8
Idiopathic subglottic stenosis in a young female patient.一名年轻女性患者的特发性声门下狭窄。
BMJ Case Rep. 2021 May 24;14(5):e241525. doi: 10.1136/bcr-2020-241525.
9
Successful management of subglottic stenosis in pregnancy.成功管理妊娠期声门下狭窄。
BMJ Case Rep. 2021 Mar 24;14(3):e236466. doi: 10.1136/bcr-2020-236466.
10
Pregnancy-associated idiopathic laryngotracheal stenosis: presentation, management and results of surgical treatment.妊娠相关特发性喉气管狭窄:临床表现、治疗及手术治疗结果
Eur J Cardiothorac Surg. 2021 Jan 4;59(1):122-129. doi: 10.1093/ejcts/ezaa296.