Tasaki Ayako, Fukuda Akihiro, Kudo Akiko, Nishikawa Emiko, Koumatsu Nobuchika, Wada Megumi, Okita Jun, Maruo Misaki, Uchida Hiroki, Nakata Takeshi, Itani Kazuhito, Shibata Hirotaka
Department of Endocrinology, Metabolism, Rheumatology and Nephrology, Faculty of Medicine, Oita University, Oita, Japan.
Division of Haematology, Faculty of Medicine, Oita University, Oita, Japan.
Nephrology (Carlton). 2025 Feb;30(2):e70003. doi: 10.1111/nep.70003.
A 73-year-old Japanese man with chronic kidney disease had no history of abnormal clotting or bleeding. Six days after receiving his third dose of the severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) vaccine (BNT162b2; Pfizer/BioNTech), blood tests showed a marked prolongation of the prothrombin time-international normalised ratio and activated partial thromboplastin time, as well as a decrease in factor V (FV) activity. Three months later, he required dialysis owing to worsening heart and renal failure. After supplementation with FV, a flexible double-lumen catheter was inserted, and haemodialysis was initiated without the use of anticoagulants. The patient was found to be positive for FV inhibitors and was diagnosed with autoimmune acquired factor V deficiency (AiFVD). AiFVD is a rare autoimmune disease in which factor V inhibitors decrease FV activity. The patient did not undergo immunosuppressive therapy because he did not have severe bleeding symptoms, and he is currently able to continue dialysis without causing fatal bleeding. FV inhibitors can be induced by bovine thrombin, surgery, and infection, but have also been detected after SARS-CoV-2 infection. The development of various acquired coagulation factor inhibitors has been reported after SARS-CoV-2 infection or vaccination, but there have been no reports of AiFVD due to SARS-CoV-2 vaccination. To the best of our knowledge, this is the first report of AiFVD probably associated with SARS-CoV-2 vaccination. Although AiFVD is rare, physicians should be aware of its possibility after SARS-CoV-2 vaccination.
一名73岁的日本男性,患有慢性肾脏病,既往无异常凝血或出血史。在接种第三剂严重急性呼吸综合征冠状病毒2(SARS-CoV-2)疫苗(BNT162b2;辉瑞/生物新技术公司)6天后,血液检查显示凝血酶原时间-国际标准化比值和活化部分凝血活酶时间显著延长,以及因子V(FV)活性降低。3个月后,由于心脏和肾衰竭加重,他需要进行透析。补充FV后,插入了一根可弯曲的双腔导管,并在不使用抗凝剂的情况下开始进行血液透析。该患者FV抑制物检测呈阳性,被诊断为自身免疫性获得性因子V缺乏症(AiFVD)。AiFVD是一种罕见的自身免疫性疾病,其中因子V抑制物会降低FV活性。该患者未接受免疫抑制治疗,因为他没有严重出血症状,目前能够继续透析而不引起致命性出血。FV抑制物可由牛凝血酶、手术和感染诱发,但在SARS-CoV-2感染后也有检测到。在SARS-CoV-2感染或接种疫苗后,已有各种获得性凝血因子抑制物产生的报道,但尚无因SARS-CoV-2疫苗接种导致AiFVD的报道。据我们所知,这是首例可能与SARS-CoV-2疫苗接种相关的AiFVD报告。尽管AiFVD罕见,但医生在SARS-CoV-2疫苗接种后应意识到其可能性。