Congenital Uterine Anomaly with Concurrent Longitudinal and Transverse Vaginal Septa: Presentation of Two Cases.

INTRODUCTION

Didelphic and septate uteri are congenital uterine anomalies caused by the failure of fusion of the Müllerian ducts or resorption of the median septum after fusion, respectively. These can occasionally be associated with a longitudinal vaginal septum. The combination with a transverse vaginal septum is rare, leads to menstrual obstruction, and presents with severe abdominal pain in early adolescence.

CASES

We present the cases of two 12-year-old girls presenting with a uterine anomaly and concomitant longitudinal vaginal septum and hematocolpos due to the presence of a transverse vaginal septum.

DISCUSSION/CONCLUSION: Congenital uterine anomalies can coexist with a longitudinal septum and rarely with a transverse vaginal septum causing obstruction. Early diagnosis and surgical correction of a transverse vaginal septum are decisive for the relief of symptoms and the prevention of future complications. Physicians should always consider the presence of complex congenital anomalies in cases of menstrual obstruction. The coexistence of uterine and vaginal anomalies in this study is not adequately described by the existing classification systems, underlining the need for a more inclusive classification system.

CATEGORIES

Obstetrics & Gynecology, Pediatrics, Pediatric & Adolescent Gynecology.