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骨髓纤维化伴心脏压塞的心包造血

Pericardial haematopoiesis with tamponade in myelofibrosis.

作者信息

Haedersdal C, Hasselbalch H, Devantier A, Saunamäki K

出版信息

Scand J Haematol. 1985 Mar;34(3):270-3. doi: 10.1111/j.1600-0609.1985.tb02791.x.

DOI:10.1111/j.1600-0609.1985.tb02791.x
PMID:3992193
Abstract

A 52-year-old male with idiopathic myelofibrosis of 8 years' duration developed pericardial tamponade during recovery from acute tubular interstitial nephropathia following septicaemia. Splenectomy had been performed 7 yr previously. The tamponade was relieved by pericardiocentesis and its recurrence was prevented by a minor pericardiectomy. Pathological examination, including staining for factor VIII-positive cells, demonstrated extramedullary haematopoiesis in the pericardium. In patients with myelofibrosis and increased silhouette on X-ray film, with or without clinical heart failure, echocardiographic examination is recommended in order to identify a possible pericardial effusion.

摘要

一名患有8年特发性骨髓纤维化的52岁男性,在败血症后急性肾小管间质性肾病恢复期间发生了心包填塞。7年前已行脾切除术。通过心包穿刺术缓解了填塞,并通过小型心包切除术预防了其复发。病理检查,包括对VIII因子阳性细胞进行染色,显示心包存在髓外造血。对于骨髓纤维化且X线胸片上心影增大的患者,无论有无临床心力衰竭,建议进行超声心动图检查以确定是否可能存在心包积液。

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引用本文的文献

1
Cardiac complications in a patient affected by systemic mastocytosis and primitive myelofibrosis: A case report.系统性肥大细胞增多症和原发性骨髓纤维化患者的心脏并发症:一例报告
Clin Case Rep. 2021 Nov 12;9(11):e04972. doi: 10.1002/ccr3.4972. eCollection 2021 Nov.
2
Extramedullary haematopoiesis presenting with cardiac tamponade in a patient with polycythaemia vera.真性红细胞增多症患者出现心脏压塞的髓外造血。
BMJ Case Rep. 2017 Aug 10;2017:bcr-2017-221316. doi: 10.1136/bcr-2017-221316.
3
Helical tomotherapy for extramedullary hematopoiesis involving the pericardium in a patient with chronic myeloid leukemia.
螺旋断层放疗治疗累及心包的慢性髓性白血病患者骨髓外造血。
Jpn J Radiol. 2010 Jul;28(6):476-8. doi: 10.1007/s11604-010-0452-y. Epub 2010 Jul 27.