Liu Jing, Li Wenqi, Jiao Ran, Liu Zhigang, Zhang Tiantian, Chai Dan, Meng Lingxin, Yang Zhongyi, Liu Yuming, Wu Hongliang, Gu Xiaoting, Li Xiaohe, Yang Cheng
State Key Laboratory of Medicinal Chemical Biology, College of Pharmacy, Nankai University, Haihe Education Park, 38 Tongyan Road, Tianjin, 300353, China.
Department of Anesthesiology, National Cancer Center/National Clinical Research Center for Cancer/Cancer Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, No. 17 Nanli, Panjiayuan, Chaoyang District, Beijing, China.
Mol Med. 2025 Feb 11;31(1):55. doi: 10.1186/s10020-025-01093-w.
Cardiac fibrosis is significant global health problem, which is associated with numerous cardiovascular diseases, and ultimately leads to the progression to heart failure. β-adrenergic receptor (β-AR) overactivation play a role in the development of cardiac fibrosis. Miglustat (Mig) has shown anti-fibrosis effects in multiple fibrotic diseases. However, it is unclear whether and how Mig can ameliorate cardiac fibrosis induced by β-AR overactivation.
In vivo, mice were injected with isoproterenol (ISO) to induce cardiac fibrosis and treated with Mig. In vitro, primary cardiac fibroblasts were stimulated by ISO and treated with Mig. Levels of cardiac fibrosis, cardiac dysfunction, activation of cardiac fibroblasts were evaluated by real-time polymerase chain reaction, western blots, sirius red staining, immunohistochemistry staining and echocardiography. Through GEO data and knockdown UDP-glucose ceramide glycosyltransferase (UGCG) in primary cardiac fibroblasts, whether Mig alleviates cardiac fibrosis by targeting UGCG was explored.
The results indicated that Mig alleviated ISO-induced cardiac dysfunction. Consistently, Mig also suppressed ISO-induced cardiac fibrosis. Moreover, Mig attenuated ISO-induced cardiac fibroblasts (CFs) activation. To identify the protective mechanism of Mig on cardiac fibrosis, several classical β-AR downstream signaling pathways, including ERK, STAT3, Akt and GSK3β, were further analyzed. As expected, ISO activated the ERK, STAT3, Akt and GSK3β in both CFs and mouse hearts, but this effect was reversed pretreated with Mig. Besides, Mig ameliorates ISO-induced cardiac fibrosis by targeting UDP-glucose ceramide glycosyltransferase (UGCG) in CFs.
Mig ameliorates β-AR overactivation-induced cardiac fibrosis by inhibiting ERK, STAT3, Akt and GSK3β signaling and UGCG may be a potential target for the treatment of cardiac fibrosis.
心脏纤维化是一个重大的全球健康问题,与多种心血管疾病相关,最终会导致心力衰竭的进展。β-肾上腺素能受体(β-AR)过度激活在心脏纤维化的发展中起作用。米格列醇(Mig)已在多种纤维化疾病中显示出抗纤维化作用。然而,尚不清楚Mig是否以及如何改善由β-AR过度激活诱导的心脏纤维化。
在体内,给小鼠注射异丙肾上腺素(ISO)以诱导心脏纤维化,并给予Mig治疗。在体外,用ISO刺激原代心脏成纤维细胞并给予Mig治疗。通过实时聚合酶链反应、蛋白质免疫印迹、天狼星红染色、免疫组织化学染色和超声心动图评估心脏纤维化水平、心脏功能障碍、心脏成纤维细胞的激活情况。通过基因表达综合数据库(GEO)数据以及在原代心脏成纤维细胞中敲低UDP-葡萄糖神经酰胺糖基转移酶(UGCG),探讨Mig是否通过靶向UGCG减轻心脏纤维化。
结果表明Mig减轻了ISO诱导的心脏功能障碍。同样,Mig也抑制了ISO诱导的心脏纤维化。此外,Mig减弱了ISO诱导的心脏成纤维细胞(CFs)激活。为了确定Mig对心脏纤维化的保护机制,进一步分析了几个经典的β-AR下游信号通路,包括细胞外调节蛋白激酶(ERK)、信号转导和转录激活因子3(STAT3)、蛋白激酶B(Akt)和糖原合成酶激酶3β(GSK3β)。正如预期的那样,ISO激活了CFs和小鼠心脏中的ERK、STAT3、Akt和GSK3β,但用Mig预处理可逆转这种作用。此外,Mig通过靶向CFs中的UDP-葡萄糖神经酰胺糖基转移酶(UGCG)改善ISO诱导的心脏纤维化。
Mig通过抑制ERK、STAT3、Akt和GSK3β信号通路改善β-AR过度激活诱导的心脏纤维化,UGCG可能是治疗心脏纤维化的一个潜在靶点。