Ohmura Yoshiaki, Takeda Yutaka, Katsura Yoshiteru, Shinke Go, Kinoshita Mitsuru, Yamaura Minami, Fukumoto Yuko, Hiraki Masayuki, Sugimura Keijiro, Masuzawa Toru, Hata Taishi, Kashiwazaki Masaki, Tanemura Masahiro, Sudo Yoshiko, Murata Kohei
Dept. of Surgery, Rinku General Medical Center.
Gan To Kagaku Ryoho. 2024 Dec;51(13):1592-1594.
Retroperitoneal leiomyosarcoma is a rare disease, and the prognosis is relatively poor. Here, we report a case in which radical resection of retroperitoneal leiomyosarcoma was possible with combined resection and reconstruction of the inferior vena cava and left renal vein. An 81-year-old patient was referred to our hospital for treatment of a retroperitoneal tumor. After detailed examination, a 5 cm-sized hypervascular solid tumor with invasion from the inferior vena cava(IVC)to the left renal vein(LRV)and tumor thrombus was found. The resection was performed, in which the IVC and LRV were resected together, and IVC was anastomosed end-to-end, and LRV stump and IVC were anastomosed end-to-side. The pathological diagnosis was leiomyosarcoma, and the patient has been undergoing follow-up observation for 1.5 years, with no recurrence. Retroperitoneal leiomyosarcoma is a rare disease, and the only treatment is complete resection of the tumor, including IVC. Even if complete resection is performed, the prognosis is poor, however, there have been a small number of reported cases of long-term survival after complete resection, so aggressive treatment is recommended.
腹膜后平滑肌肉瘤是一种罕见疾病,预后相对较差。在此,我们报告一例通过联合切除及重建下腔静脉和左肾静脉成功进行腹膜后平滑肌肉瘤根治性切除的病例。一名81岁患者因腹膜后肿瘤被转诊至我院治疗。经过详细检查,发现一个5厘米大小的高血供实性肿瘤,侵犯范围从下腔静脉至左肾静脉,并伴有肿瘤血栓形成。手术切除时,将下腔静脉和左肾静脉一并切除,下腔静脉进行端端吻合,左肾静脉残端与下腔静脉进行端侧吻合。病理诊断为平滑肌肉瘤,患者已接受1.5年的随访观察,无复发。腹膜后平滑肌肉瘤是一种罕见疾病,唯一的治疗方法是完整切除肿瘤,包括下腔静脉。即使进行了完整切除,预后仍较差,不过,已有少数完整切除后长期生存的病例报道,因此建议积极治疗。