Of Zebrafish, Mice, and Men: Identifying New Biology and Developing New Treatments for Erythropoietic Protoporphyria.
作者信息
Molleston Jean P, Jarasvaraparn Chaowapong
机构信息
Pediatric Gastroenterology, Hepatology and Nutrition, Riley Hospital for Children at Indiana University Health, Indianapolis, Indiana.
Department of Pediatrics, Indiana University School of Medicine/Riley Hospital for Children, Indianapolis, Indiana.
出版信息
Cell Mol Gastroenterol Hepatol. 2025;19(6):101477. doi: 10.1016/j.jcmgh.2025.101477. Epub 2025 Feb 22.
Abstract
摘要
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本文引用的文献
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The Histamine Pathway is a Target to Treat Hepatic Experimental Erythropoietic Protoporphyria.组胺途径是治疗肝脏实验性红细胞生成性原卟啉症的一个靶点。
Cell Mol Gastroenterol Hepatol. 2025;19(6):101463. doi: 10.1016/j.jcmgh.2025.101463. Epub 2025 Jan 15.
2
FXR in liver physiology: Multiple faces to regulate liver metabolism.FXR 在肝脏生理学中的作用：调节肝脏代谢的多面手。
Biochim Biophys Acta Mol Basis Dis. 2021 Jul 1;1867(7):166133. doi: 10.1016/j.bbadis.2021.166133. Epub 2021 Mar 24.
3
Cimetidine/lactulose therapy ameliorates erythropoietic protoporphyria-related liver injury.西咪替丁/乳果糖疗法可改善红细胞生成性原卟啉症相关肝损伤。
Clin J Gastroenterol. 2017 Oct;10(5):452-458. doi: 10.1007/s12328-017-0760-1. Epub 2017 Jul 4.
4
Clinical, Biochemical, and Genetic Characterization of North American Patients With Erythropoietic Protoporphyria and X-linked Protoporphyria.北美红细胞生成性原卟啉症和X连锁原卟啉症患者的临床、生化及遗传学特征
JAMA Dermatol. 2017 Aug 1;153(8):789-796. doi: 10.1001/jamadermatol.2017.1557.
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