Srivillibhuthur Manasa, Yu Tammy, Li Martin, Mader Ingrid, Arikan Pinar
Internal Medicine Residency Warren Alpert Medical School of Brown University.
Warren Alpert Medical School of Brown University.
J Brown Hosp Med. 2023 Jul 2;2(3):77572. doi: 10.56305/001c.77572. eCollection 2023.
A 67-year-old man with a history of hypertension, hyperlipidemia, coronary artery disease, and former smoking presented with fatigue, lower extremity edema, and a new tremor over the course of one month. Workup was notable for hypokalemia, metabolic alkalosis, and extremely elevated adrenocorticotropic hormone (ACTH) and cortisol levels. He was ultimately diagnosed with ectopic Cushing's syndrome (CS) secondary to new metastatic small cell lung carcinoma. About 5-10% of CS cases are caused by ectopic ACTH production. The most commonly implicated malignancies are small cell lung cancer (SCLC) and neuroendocrine tumors, with SCLC accounting for up to three-fourths of cases. ACTH production is a poor prognostic sign in SCLC, associated with more extensive disease and decreased response to first-line treatment. Tumor-associated ACTH production is often so rapid that patients do not have time to develop classic Cushingoid physical exam findings, instead presenting with acute-onset hyperglycemia, pseudohyperaldosteronism, and generalized weakness. Prompt diagnosis and treatment are essential to improve outcomes.
一名67岁男性,有高血压、高脂血症、冠状动脉疾病病史,既往吸烟,在一个月内出现疲劳、下肢水肿和新发震颤。检查发现有低钾血症、代谢性碱中毒,促肾上腺皮质激素(ACTH)和皮质醇水平极度升高。他最终被诊断为继发于新发性转移性小细胞肺癌的异位库欣综合征(CS)。约5%-10%的CS病例由异位ACTH分泌引起。最常涉及的恶性肿瘤是小细胞肺癌(SCLC)和神经内分泌肿瘤,其中SCLC占病例的四分之三。ACTH分泌在SCLC中是预后不良的标志,与更广泛的疾病和对一线治疗反应降低有关。肿瘤相关的ACTH分泌通常非常迅速,以至于患者没有时间出现典型的库欣样体格检查发现,而是表现为急性发作的高血糖、假性醛固酮增多症和全身无力。及时诊断和治疗对于改善预后至关重要。