利德尔综合征患者的心脏移植
Heart Transplantation in a Patient With Liddle Syndrome.
作者信息
Gohri Jay, Bakhle Rahul, Calhoun Avery E, Sajja Aparna, Bhatt Kunal N
机构信息
JSS Medical College, Karnataka, India.
Medical College Baroda SSGH, Gujarat, India.
出版信息
JACC Case Rep. 2025 Mar 5;30(5):103079. doi: 10.1016/j.jaccas.2024.103079.
Abstract
Liddle syndrome is characterized by hypertension, hypokalemia, and metabolic alkalosis. This paper presents the case of a 29-year-old man with Liddle syndrome complicated by stage D heart failure and stage 4 chronic kidney disease. Despite appropriate management, this patient developed refractory cardiogenic shock, ultimately requiring mechanical circulatory support with venoarterial extracorporeal membrane oxygenation and expedited heart transplant listing.
摘要
利德尔综合征的特征为高血压、低钾血症和代谢性碱中毒。本文介绍了一名29岁患有利德尔综合征并伴有D期心力衰竭和4期慢性肾脏病的男性病例。尽管进行了适当的治疗，该患者仍出现难治性心源性休克，最终需要采用静脉-动脉体外膜肺氧合进行机械循环支持并加快心脏移植等待名单排序。
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