Abdul Khalek Jad, El Rassi Christophe, Abou Mansour Maria, Sleem Bshara, El Rassi Issam, Bitar Fadi, Arabi Mariam
Faculty of Medicine, American University of Beirut Medical Center, Beirut, Lebanon.
Department of Pediatric Cardiac Surgery, Al Jalila Children's Specialty Hospital, Dubai, United Arab Emirates.
Front Cardiovasc Med. 2025 Mar 4;12:1531754. doi: 10.3389/fcvm.2025.1531754. eCollection 2025.
Cor Triatriatum is a congenital anomaly characterized by the abnormal presence of a fibromuscular junction in one of the atria, as seen on echocardiography. This anomaly can lead to major hemodynamic problems and obstruction of blood flow. This study aims to explore the risk factors, diagnostic modalities, and surgical interventions used to tackle this congenital anomaly at a tertiary care center over an 18-year period.
Medical records of congenital heart disease patients at the Children's Heart Center at the American University of Beirut Medical Center between 2006 and 2024 were retrospectively reviewed. Data collection included demographic characteristics, clinical outcomes, hospitalization details, and surgical treatment. Ethical approval was obtained, and descriptive statistics were employed for data analysis using SAS 9.4.
At our center, 7 patients were diagnosed with Cor Triatriatum, with a median age of 5 months. 4 of the patients were female, 3 were males, and the median hospital stay was 7 days. All patients were diagnosed with Cor Triatriatum Sinister, and respiratory symptoms were prevalent. Pulmonary vein abnormalities were observed in 4 ouf of 7 (57.1%) patients and atrial septal defects in 2 out of 7 patients (28.5%). Surgery resulted in successful membrane resection for all operated patients, with significant symptom improvement postoperatively.
Cor Triatriatum is a rare congenital anomaly requiring early detection and diagnosis. Surgical intervention remains the mainstay of treatment, with favorable outcomes when performed promptly. Larger studies are recommended to optimize management strategies and improve long-term outcomes for affected patients.
三房心是一种先天性异常，其特征是在心房之一中存在纤维肌性连接，这在超声心动图上可见。这种异常可导致严重的血流动力学问题和血流梗阻。本研究旨在探讨一家三级医疗中心在18年期间用于处理这种先天性异常的危险因素、诊断方式和手术干预措施。
回顾性分析了2006年至2024年期间贝鲁特美国大学医学中心儿童心脏中心先天性心脏病患者的病历。数据收集包括人口统计学特征、临床结局、住院细节和手术治疗。获得了伦理批准，并使用SAS 9.4进行描述性统计分析数据。
在我们中心，7例患者被诊断为三房心，中位年龄为5个月。其中4例为女性，3例为男性，中位住院时间为7天。所有患者均被诊断为左位三房心，且呼吸道症状普遍。7例患者中有4例（57.1%）观察到肺静脉异常，7例患者中有2例（28.5%）观察到房间隔缺损。手术使所有接受手术的患者成功进行了膜切除，术后症状有显著改善。
三房心是一种罕见的先天性异常，需要早期发现和诊断。手术干预仍然是主要的治疗方法，及时进行手术可取得良好的效果。建议进行更大规模的研究以优化管理策略并改善受影响患者的长期结局。
