Manocchio Nicola, Magro Valerio Massimo, Massaro Livio, Sorbino Andrea, Ljoka Concetta, Foti Calogero
Physical and Rehabilitation Medicine, Tor Vergata University, 00133 Rome, Italy.
Biomedicines. 2025 Mar 17;13(3):726. doi: 10.3390/biomedicines13030726.
Hashimoto's encephalopathy (HE), also known as steroid-responsive encephalopathy associated with autoimmune thyroiditis (SREAT), is an autoimmune disorder with heterogeneous presentation that poses diagnostic challenges. This review synthesizes the current literature to clarify the clinical, laboratory, and radiological features of SREAT/HE, including the diagnostic utility of thyroid peroxidase (TPO) antibodies, cerebrospinal fluid (CSF) abnormalities, and neuroimaging findings. Cognitive impairment and behavioral changes are common in HE, but specific manifestations vary widely, which can lead to misdiagnosis. While elevated TPO antibodies are frequently observed, a direct causal relationship with HE is unlikely, and their presence may indicate a general state of autoimmunity. Corticosteroids remain the cornerstone of treatment, although responses vary, and alternative immunosuppressive agents or intravenous immunoglobulin may be needed in some cases. Evidence regarding rehabilitation for people affected by HE is limited, but neurorehabilitation strategies adapted from other neurological conditions, including cognitive re-education (CR), physical therapy, and psychosocial support, may be beneficial. Further research is needed to elucidate the underlying mechanisms of SREAT, refine the diagnostic criteria, and develop more targeted and effective therapies, including rehabilitation strategies, for this debilitating neurological disorder.
桥本脑病(HE),也称为与自身免疫性甲状腺炎相关的类固醇反应性脑病(SREAT),是一种临床表现多样的自身免疫性疾病,给诊断带来了挑战。本综述综合了当前文献,以阐明SREAT/HE的临床、实验室和影像学特征,包括甲状腺过氧化物酶(TPO)抗体的诊断效用、脑脊液(CSF)异常及神经影像学表现。认知障碍和行为改变在HE中很常见,但具体表现差异很大,这可能导致误诊。虽然经常观察到TPO抗体升高,但与HE的直接因果关系不太可能,其存在可能表明自身免疫的一般状态。皮质类固醇仍然是治疗的基石,尽管反应各不相同,在某些情况下可能需要使用其他免疫抑制剂或静脉注射免疫球蛋白。关于HE患者康复的证据有限,但借鉴其他神经系统疾病的神经康复策略,包括认知再教育(CR)、物理治疗和心理社会支持,可能会有所帮助。需要进一步研究以阐明SREAT的潜在机制,完善诊断标准,并为这种使人衰弱的神经系统疾病开发更有针对性和有效的治疗方法,包括康复策略。