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巨大升主动脉瘤:一例罕见病例报告。

Giant ascending aortic aneurysm: A rare case report.

作者信息

Mitsali Thirafi, Dewi Dian Komala

机构信息

Faculty of Medicine University of Padjadjaran, Dr. Hasan Sadikin General Hospital, Department of Radiology, Pasteur No.38, Bandung City, West Java 40161, Indonesia.

出版信息

Radiol Case Rep. 2025 Mar 18;20(6):2797-2801. doi: 10.1016/j.radcr.2025.02.030. eCollection 2025 Jun.

DOI:10.1016/j.radcr.2025.02.030
PMID:40176978
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11964594/
Abstract

A giant ascending aortic aneurysm (AscAA), defined as an aneurysm larger than 10 cm, is a rare and potentially life-threatening condition that often remains asymptomatic until it reaches a critical size. Atherosclerosis is the most common cause in elderly patients, and imaging plays a crucial role in diagnosis and management. In this case, a 72-year-old man presented with intermittent sharp chest pain radiating to the back, progressive hoarseness over 5 years, and shortness of breath. Imaging revealed a 12.51 cm × 11.27 cm × 10.0 cm saccular aneurysm with calcified plaques, consistent with a Stanford Type A aortic aneurysm and underlying atherosclerosis. Surgical intervention remains the only definitive treatment, although it carries significant risks. Early diagnosis, timely surgical intervention, and postoperative surveillance are critical in improving patient outcomes for this high-risk condition.

摘要

巨大升主动脉瘤(AscAA)定义为直径大于10厘米的动脉瘤,是一种罕见且可能危及生命的疾病,通常在达到临界大小之前一直无症状。动脉粥样硬化是老年患者最常见的病因,影像学在诊断和管理中起着关键作用。在本病例中,一名72岁男性出现间歇性尖锐胸痛并放射至背部,5年来声音逐渐嘶哑,伴有呼吸急促。影像学检查发现一个12.51厘米×11.27厘米×10.0厘米的囊状动脉瘤,伴有钙化斑块,符合斯坦福A型主动脉瘤及潜在的动脉粥样硬化。手术干预仍然是唯一的确定性治疗方法,尽管它具有重大风险。早期诊断、及时的手术干预和术后监测对于改善这种高危疾病患者的预后至关重要。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/b89aa55d79cc/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/6bdfbb8bc7ca/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/40a75c8e4613/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/b89aa55d79cc/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/6bdfbb8bc7ca/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/40a75c8e4613/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0a2e/11964594/b89aa55d79cc/gr3.jpg

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本文引用的文献

1
The ascending aortic aneurysm: When to intervene?升主动脉瘤:何时进行干预?
Int J Cardiol Heart Vasc. 2015 Jan 20;6:91-100. doi: 10.1016/j.ijcha.2015.01.009. eCollection 2015 Mar 1.
2
2022 ACC/AHA Guideline for the Diagnosis and Management of Aortic Disease: A Report of the American Heart Association/American College of Cardiology Joint Committee on Clinical Practice Guidelines.2022 ACC/AHA 血管疾病诊断与管理指南:美国心脏协会/美国心脏病学会联合临床实践指南委员会的报告。
Circulation. 2022 Dec 13;146(24):e334-e482. doi: 10.1161/CIR.0000000000001106. Epub 2022 Nov 2.
3
A Case Report of Giant Ascending Aortic Aneurysm: Role of Multimodality Imaging.
巨大升主动脉瘤病例报告:多模态成像的作用
Aorta (Stamford). 2021 Jun;9(3):106-109. doi: 10.1055/s-0041-1730005. Epub 2021 Oct 12.
4
The Largest Reported Giant Ascending Aortic Aneurysm Presented with Superior Vena Cava Syndrome.最大的报道巨型升主动脉瘤伴上腔静脉综合征。
Braz J Cardiovasc Surg. 2020 Oct 29;35(5):834-837. doi: 10.21470/1678-9741-2019-0151.
5
Unusual non progressive idiopathic giant ascending aortic aneurysm-A rarity.罕见的非进行性特发性升主动脉巨大动脉瘤——一种罕见病。
Int J Surg Case Rep. 2016;25:203-6. doi: 10.1016/j.ijscr.2016.06.049. Epub 2016 Jul 1.
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2010 ACCF/AHA/AATS/ACR/ASA/SCA/SCAI/SIR/STS/SVM Guidelines for the diagnosis and management of patients with thoracic aortic disease. A Report of the American College of Cardiology Foundation/American Heart Association Task Force on Practice Guidelines, American Association for Thoracic Surgery, American College of Radiology,American Stroke Association, Society of Cardiovascular Anesthesiologists, Society for Cardiovascular Angiography and Interventions, Society of Interventional Radiology, Society of Thoracic Surgeons,and Society for Vascular Medicine.2010年美国心脏病学会基金会/美国心脏协会/美国胸外科医师协会/美国放射学会/美国卒中协会/心血管麻醉医师协会/心血管造影和介入学会/介入放射学会/胸外科医师学会/血管医学学会胸主动脉疾病患者诊断和管理指南。美国心脏病学会基金会/美国心脏协会实践指南工作组、美国胸外科协会、美国放射学会、美国卒中协会、心血管麻醉医师协会、心血管造影和介入学会、介入放射学会、胸外科医师学会及血管医学学会报告。
J Am Coll Cardiol. 2010 Apr 6;55(14):e27-e129. doi: 10.1016/j.jacc.2010.02.015.