External jugular vein pseudoaneurysm in a case of sickle cell anemia.

Aneurysm and pseudoaneurysm of venous system are uncommon. Their association with external jugular vein (EJV) is relatively rare. There is no reported case of association of EJV aneurysm in a patient with sickle cell anemia. Small aneurysm/pseudoaneurysm, if asymptomatic, are managed conservatively. However, if large or thrombosed, surgical excision is the treatment of choice. Their association with sickle cell anemia makes it a challenge not only for the surgeon, but also for the anesthetist, and requires a planned and disciplinary approach.