Inoue Fumiya, Ono Shin, Ueda Hideaki
Pediatric Cardiology, Kanagawa Children's Medical Center, Yokohama, JPN.
Cureus. 2025 Mar 19;17(3):e80824. doi: 10.7759/cureus.80824. eCollection 2025 Mar.
Plastic bronchitis is a severe complication following the Fontan procedure, characterized by the formation of tracheal casts, leading to respiratory failure. No established treatment exists for post-surgical plastic bronchitis. We present the case of a three-year-old boy with hypoplastic left heart syndrome who developed plastic bronchitis two years after the Fontan procedure. Despite initial treatments, his condition did not improve until catheterization was performed to place a stent in the left pulmonary artery and embolize aortopulmonary collateral vessels. This combined approach resulted in significant clinical improvement and no recurrence until 17 months. Elevated pulmonary venous pressure can lead to increased mucin secretion from the tracheal epithelium; reducing this pressure may be effective for treating plastic bronchitis. Our case demonstrates the successful application of simultaneous stenting and coil embolization, resulting in a rapid decrease in pulmonary venous pressure and an improvement in the patient's condition. This combined approach may offer a promising therapeutic option for managing plastic bronchitis after the Fontan procedure.
塑料支气管炎是Fontan手术后的一种严重并发症,其特征是形成气管铸型,导致呼吸衰竭。目前尚无针对术后塑料支气管炎的确立治疗方法。我们报告一例三岁患有左心发育不全综合征的男孩,其在Fontan手术后两年发生了塑料支气管炎。尽管进行了初始治疗,但直到进行导管插入术以在左肺动脉放置支架并栓塞体肺侧支血管后,他的病情才有所改善。这种联合方法导致了显著的临床改善,并且在17个月内未复发。肺静脉压力升高可导致气管上皮粘蛋白分泌增加;降低这种压力可能对治疗塑料支气管炎有效。我们的病例证明了同时进行支架置入和弹簧圈栓塞的成功应用,导致肺静脉压力迅速降低和患者病情改善。这种联合方法可能为Fontan手术后管理塑料支气管炎提供一种有前景的治疗选择。