Sarafoleanu Caius-Codrut, Badea Florentina-Carmen, Georgescu Alina-Maria, Musat Gabriela-Cornelia, Andrei Anica, Tanase Ionut
Department of Otorhinolaryngology, "Carol Davila" University of Medicine and Pharmacy, 050474 Bucharest, Romania.
Department of Otorhinolaryngology, "Sfanta Maria" Clinical Hospital, 011172 Bucharest, Romania.
Medicina (Kaunas). 2025 Mar 25;61(4):585. doi: 10.3390/medicina61040585.
Rosai-Dorfman disease (RDD) is a rare proliferative disorder characterized by an overproduction of a type of immune cell called histiocytes, with unknown etiology. Although extranodal involvement is not uncommon, it is rarely seen within the nose. The available data are limited, and currently, there are no established guidelines for managing RDD. Different therapeutic options have been described, including corticosteroids, surgery, radiotherapy, or chemotherapy. This study aims to evaluate the potential benefit of radiotherapy in patients with nasal Rosai-Dorfman disease to improve the current diagnostic and therapeutic management. Herein, we report the case of a 54-year-old female patient with nasal RDD refractory to systemic corticosteroid therapy and transnasal endoscopic resection. She received fractionated low-dose radiotherapy with a total dose of 30 cGy administered in 2 cGy daily fractions. Complete remission was achieved, highlighting the potential role of radiotherapy as an effective therapeutic option for relapsing or steroid-refractory cases. This is one of the few well-documented cases reported with nasal Rosai-Dorfman disease treated with radiotherapy. Ongoing research on novel therapies offers hope for improved outcomes in relapsing cases that fail to respond to conventional treatments.
罗萨伊-多夫曼病(RDD)是一种罕见的增殖性疾病,其特征是一种名为组织细胞的免疫细胞过度产生,病因不明。虽然结外受累并不罕见,但在鼻腔内很少见。现有数据有限,目前尚无针对RDD的既定管理指南。已描述了不同的治疗选择,包括皮质类固醇、手术、放疗或化疗。本研究旨在评估放疗对鼻腔罗萨伊-多夫曼病患者的潜在益处,以改善当前的诊断和治疗管理。在此,我们报告一例54岁女性鼻腔RDD患者,该患者对全身皮质类固醇治疗和经鼻内镜切除均无效。她接受了分次低剂量放疗,总剂量为30 cGy,每日分次给予2 cGy。实现了完全缓解,突出了放疗作为复发性或类固醇难治性病例有效治疗选择的潜在作用。这是少数有详细记录的鼻腔罗萨伊-多夫曼病放疗病例之一。正在进行的新型疗法研究为复发性病例对传统治疗无反应的改善结果带来了希望。