Kim Min Jee, Yang Jiyoul, Song Jin Woo
Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.
Korean J Intern Med. 2025 May;40(3):458-467. doi: 10.3904/kjim.2024.244. Epub 2025 Apr 30.
BACKGROUND/AIMS: Patients with acute exacerbation of idiopathic pulmonary fibrosis (AE-IPF) typically have a poor prognosis; however, no effective treatment is available. In recent years, several retrospective studies have suggested the clinical benefits of direct hemoperfusion with a polymyxin B-immobilized fiber column (PMX-DHP) in patients with AE-IPF. Herein, we aimed to investigate the efficacy and safety of PMX-DHP treatment in patients with AE-IPF.
Patients diagnosed with AE-IPF (n = 10) with a partial pressure of oxygen to fraction of inspiratory oxygen ratio (P/F ratio) > 100 were prospectively enrolled at a single center. PMX-DHP was performed twice for 6 hours (at 24-h intervals) at a flow rate of 80-100 mL/min, and steroid pulse therapy was concurrently administered (500 mg of methylprednisolone for 3 d).
The mean patient age was 67 years, and 80.0% were male. During the follow-up (median, 42.5 d; interquartile range, 16.0-174.0 d), seven (70.0%) patients died (including two who underwent transplantation); the in-hospital mortality rate was 70%, while the 30- and 90-day mortality rates were 50.0% and 70.0%, respectively. After 48 hours of PMX-DHP treatment, the P/F ratio improved (mean, 160.0 vs. 229.0; p = 0.054) and C-reactive protein level decreased (mean, 8.3 mg/dL vs. 3.5 mg/dL; p = 0.012). During hospitalization, no PMX-DHP-associated adverse events were observed.
Our results suggest that PMX-DHP treatment may be useful at improving oxygenation and reducing inflammation in patients with AE-IPF with acceptable safety profiles, however without affecting their prognosis.
背景/目的:特发性肺纤维化急性加重(AE-IPF)患者的预后通常较差;然而,目前尚无有效的治疗方法。近年来,多项回顾性研究表明,使用多黏菌素B固定纤维柱直接血液灌流(PMX-DHP)对AE-IPF患者具有临床益处。在此,我们旨在研究PMX-DHP治疗AE-IPF患者的疗效和安全性。
在单一中心前瞻性纳入10例诊断为AE-IPF且氧分压与吸入氧分数比(P/F比)>100的患者。以80-100 mL/min的流速进行两次PMX-DHP治疗,每次6小时(间隔24小时),同时给予类固醇脉冲疗法(3天内静脉注射500 mg甲泼尼龙)。
患者的平均年龄为67岁,80.0%为男性。在随访期间(中位数为42.5天;四分位间距为16.0-174.0天),7例(70.0%)患者死亡(包括2例接受移植的患者);住院死亡率为70%,30天和90天死亡率分别为50.0%和70.0%。PMX-DHP治疗48小时后,P/F比有所改善(平均值:160.0对229.0;p=0.054),C反应蛋白水平降低(平均值:8.3 mg/dL对3.5 mg/dL;p=0.012)。住院期间,未观察到与PMX-DHP相关的不良事件。
我们的结果表明,PMX-DHP治疗可能有助于改善AE-IPF患者的氧合和减轻炎症,安全性良好,但不影响其预后。