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血栓性血小板减少性紫癜中的浆液性视网膜脱离

Serous retinal detachments in thrombotic thrombocytopenic purpura.

作者信息

Lambert S R, High K A, Cotlier E, Benz E J

出版信息

Arch Ophthalmol. 1985 Aug;103(8):1172-4. doi: 10.1001/archopht.1985.01050080084026.

DOI:10.1001/archopht.1985.01050080084026
PMID:4040743
Abstract

Serous retinal detachments are a rare ocular complication of thrombotic thrombocytopenic purpura (TTP), with only six previous case reports in the literature. We have recently observed two patients with relapsing TTP who developed bilateral serous retinal detachments during acute exacerbations of their disease. In contrast to all but one of the previously described patients, both of our patients survived the episode during which retinal detachments occurred. Hypertension appears to contribute to the development of retinal detachments in TTP, and vigorous efforts at blood pressure control are indicated. Serous retinal detachments may be a more frequent component of chronic relapsing TTP than has been suspected.

摘要

浆液性视网膜脱离是血栓性血小板减少性紫癜(TTP)一种罕见的眼部并发症,文献中此前仅有6例病例报告。我们最近观察到2例复发性TTP患者,在疾病急性加重期出现了双侧浆液性视网膜脱离。与之前描述的除1例之外的所有患者不同,我们的2例患者在发生视网膜脱离的发作期均存活下来。高血压似乎促使TTP患者发生视网膜脱离,因此需要大力控制血压。浆液性视网膜脱离可能是慢性复发性TTP中比人们怀疑的更为常见的一个组成部分。

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引用本文的文献

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Near-complete vision recovery from bilateral serous retinal detachment associated with thrombotic thrombocytopenic purpura.双侧血清性视网膜脱离伴血栓性血小板减少性紫癜的近乎完全视力恢复。
BMJ Case Rep. 2022 Feb 7;15(2):e244030. doi: 10.1136/bcr-2021-244030.
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Retinal involvement in acute thrombotic thrombocytopenic purpura: a case report.急性血栓性血小板减少性紫癜的视网膜受累:一例报告。
BMC Ophthalmol. 2020 Nov 19;20(1):456. doi: 10.1186/s12886-020-01719-z.
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