对50名患有镰状细胞病的巴林患者及其部分父母的血液学检查结果进行评估。
Evaluation of haematological findings in 50 Bahraini patients with sickle cell disease and in some of their parents.
作者信息
Buhazza M A, Bikhazi A B, Khouri F P
出版信息
J Med Genet. 1985 Aug;22(4):293-5. doi: 10.1136/jmg.22.4.293.
Abstract
The haematological findings in 50 Bahrainis with sickle cell disease are reported. This establishes the existence of the Hb S gene in Bahrain. The mean Hb F level in the Bahraini patients was 13.8%, a value lower than that encountered in sickle cell homozygotes from Kuwait and Saudi Arabia.
摘要
报告了50名患有镰状细胞病的巴林人的血液学检查结果。这证实了巴林存在血红蛋白S基因。巴林患者的平均胎儿血红蛋白水平为13.8%，该值低于在科威特和沙特阿拉伯的镰状细胞纯合子中所观察到的值。
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