Reynard Pierre, Damien Maxime, Constant Ionescu Eugen, Thai-Van Hung
Department of Audiology and Neurotology, Civil Hospitals of Lyon, Lyon, France.
Team Clinical and Translational Exploration of Sensorineural Hearing Loss, Hearing Institute, Research Center of Pasteur Institute, Inserm U1120, Paris, France.
J Int Adv Otol. 2025 May 27;21(3):1-4. doi: 10.5152/iao.2025.241625.
The vestibular atelectasis (VA) is a very rarely reported clinical and radiological condition characterized by the collapse of the labyrinthine membrane. Clinical features include symptoms which mimic endolymphatic hydrops; bilateral forms are rarely reported in the literature. Tullio's sign was reported in a few cases. In this paper, we report an original case of bilateral fluctuating VA associated with a rare posterior semicircular canal (SSC) dehiscence variant. A 54-year-old patient presented with evolving and fluctuating bilateral vestibulopathy associated with a pressureinduced nystagmus. Vestibular assessment revealed a bilateral vestibulopathy affecting low and mid velocities, with fluctuating high-velocity impairment. Exploration of the otolithic system showed preserved saccular activity and an absence of utriculo-ocular response. Radiological evaluation demonstrated bilateral VA and a dehiscence of the right posterior SSC. We provide clinical elements to better understand this entity, and propose a new hypothesis for the presence of a previously reported Tullio sign in VA.
前庭性肺不张（VA）是一种临床和影像学表现均很少被报道的疾病，其特征为迷路膜塌陷。临床特征包括类似内淋巴积水的症状；文献中很少报道双侧形式。少数病例报告了图利奥氏征。在本文中，我们报告了一例双侧波动性VA的原始病例，该病例与一种罕见的后半规管（SSC）裂开变异有关。一名54岁患者表现为进行性和波动性双侧前庭病，伴有压力性眼球震颤。前庭评估显示双侧前庭病影响低速和中速，高速功能有波动性损害。耳石系统检查显示球囊活动正常，无椭圆囊眼反射。影像学评估显示双侧VA和右侧后半规管裂开。我们提供了临床资料以更好地理解这一实体，并对VA中先前报道的图利奥氏征的存在提出了新的假说。
