Reynolds M A, Murphy N P, Harris F
Clin Pediatr (Phila). 1985 Nov;24(11):658-9. doi: 10.1177/000992288502401116.
A case of salt-losing congenital adrenal hyperplasia with severe hyponatremic dehydration is presented. Clinical signs and symptoms of cerebral edema with elevated intracranial pressure were present. Conventional treatment was started, and after initial concern regarding future head growth and development, there was a good outcome with normal development at 1 year of age. This course is suggestive of benign intracranial hypertension. Possible mechanisms are discussed with a review of the relevant literature.
本文报告一例失盐型先天性肾上腺皮质增生症伴严重低钠血症性脱水的病例。该病例出现了伴有颅内压升高的脑水肿的临床体征和症状。开始进行常规治疗,在最初对未来头部生长发育存在担忧之后,患儿1岁时发育正常,预后良好。该病程提示为良性颅内高压。本文结合相关文献复习对可能的机制进行了讨论。