Shi Yingfeng, Li Jinqing, Zhong Qin, Chen Hui, Ma Xiaoyan, Hu Yan, Wang Yishu, Jiang Daofang, Zhou Xun, Li Xialin, Zhuang Shougang, Liu Na
Department of Nephrology, Shanghai East Hospital, Tongji University School of Medicine, Shanghai, PR China.
Department of Medicine, Rhode Island Hospital and Alpert Medical School, Brown University, Providence, Rhode Island, USA.
J Pathol. 2025 Aug;266(4-5):447-464. doi: 10.1002/path.6436. Epub 2025 Jun 20.
Peritoneal fibrosis (PF) is a serious complication contributing to ultrafiltration failure in patients undergoing peritoneal dialysis that currently lacks effective treatment strategies. Our recent studies highlighted the key role of histone deacetylase 6 (HDAC6) in the development of PF. To better understand the mechanisms underlying the involvement of HDAC6 in PF, we conducted in vivo experiments using Hdac6 KO mice and in vitro studies using human peritoneal mesothelial cells (HPMCs). Our results demonstrated that HDAC6 gene silencing improved PF and angiogenesis in vivo and altered pathological phenotypes in vitro. In Hdac6 KO mice, the key pathways regulating extracellular matrix accumulation, angiogenesis, and secretion of inflammatory cytokines (including TGFB1/SMAD3, HIF-1α/VEGFR-2/MAPK3/MAPK1, and TLR4/NF-κB pathways) were inhibited. We also identified heat shock protein 90 (HSP90) as the substrate of HDAC6 in both PF mice and HPMCs and demonstrated that HDAC6 exerted its regulatory function in PF through the deacetylation of HSP90. Overall, our study provides novel insights into the critical role of the HDAC6-HSP90 interplay in PF using Hdac6 KO mice. We identify HSP90 as an essential substrate through which HDAC6 exerts its function in PF, providing an experimental basis for the development of novel therapeutic strategies. © 2025 The Pathological Society of Great Britain and Ireland.
腹膜纤维化(PF)是腹膜透析患者超滤失败的一种严重并发症,目前缺乏有效的治疗策略。我们最近的研究强调了组蛋白去乙酰化酶6(HDAC6)在PF发生发展中的关键作用。为了更好地理解HDAC6参与PF的潜在机制,我们使用Hdac6基因敲除小鼠进行了体内实验,并使用人腹膜间皮细胞(HPMCs)进行了体外研究。我们的结果表明,HDAC6基因沉默在体内改善了PF和血管生成,并在体外改变了病理表型。在Hdac6基因敲除小鼠中,调节细胞外基质积累、血管生成和炎性细胞因子分泌的关键信号通路(包括TGFB1/SMAD3、HIF-1α/VEGFR-2/MAPK3/MAPK1和TLR4/NF-κB信号通路)受到抑制。我们还确定热休克蛋白90(HSP90)是PF小鼠和HPMCs中HDAC6的底物,并证明HDAC6通过对HSP90去乙酰化在PF中发挥其调节功能。总体而言,我们的研究利用Hdac6基因敲除小鼠对HDAC6-HSP90相互作用在PF中的关键作用提供了新的见解。我们确定HSP90是HDAC6在PF中发挥功能的必需底物,为开发新的治疗策略提供了实验依据。© 2025年英国和爱尔兰病理学会。